
Mild processing defect of porcine ÎF508-CFTR suggests that ÎF508 pigs may not develop cystic fibrosis disease
Keywords: CF; cystic fibrosis; CFTR; cystic fibrosis transmembrane conductance regulator; NBD; nucleotide binding domain; wt; wild-type; FRT; fisher rat thyroid; Porcine CFTR; ÎF508 mutation; Processing defect; Transgenic pig model;