Hipertensión arterial pulmonar en paciente con neumonía intersticial no específica y con test de vasorreactividad positivo

We present the case of a female patient diagnosed of PH with images suggestive of interstitial disease in the high resolution computed tomography and who was subsequently diagnosed of a non-specific interstitial pneumonia. It is important to stress the positive vasoreactivity test in cardiac catheterization that may indicate the presence of two independent conditions in the present case.