Unilateral superior pellucid marginal degeneration in a case with ichthyosis

A 47-year-old man with ichthyosis vulgaris presented to our hospital complaining of reduced visual acuity and ocular discomfort in the left eye. Slit-lamp biomicroscopy revealed a thinning about 2 mm from the superior limbus and superficial punctate corneal lesions in the left eyes. Corneal topography was ‘butterfly-like’ in an area of increased elevation in the left eye. Although ichthyosis vulgaris and unilateral superior pellucid marginal degeneration are both uncommon conditions, this is first report about these two conditions in studied together.