Blue rubber bleb nevus syndrome – Anaesthetic experience of prolonged bowel surgery in a twelve year old child and review

Blue rubber bleb nevus syndrome (BRBNS) is a rare hereditary disease manifested by multiple vascular malformations involving skin, mucosa and musculoskeletal system. Available literature consists of mainly airway management of such patients. We describe the perioperative anaesthetic management of a child of BBRNS with gastrointestinal bleeding disorder scheduled for resection of multiple nevi and discuss the relevant anaesthetic concerns.