The Fontan circulation and right parietal craniotomy for seizures: the challenges of adult congenital heart disease

The management of a patient who had previously undergone surgical palliation of tricuspid atresia at the age of two, and who required right parietal craniotomy for resection of seizure focus, is presented. The anesthetic considerations in patients with Fontan physiology are also presented, as well as the impact on patients undergoing neurosurgical procedures, specifically, craniotomy for seizure focus resection. The physiologic demands of modern surgical practice requires that there is a thorough understanding of the complex circulations that exist in patients with congenital heart disease.