کد مقاله | کد نشریه | سال انتشار | مقاله انگلیسی | نسخه تمام متن |
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2777220 | 1152689 | 2013 | 4 صفحه PDF | دانلود رایگان |

Wiskott–Aldrich syndrome (WAS) is a condition with variable expression, which causes persistent thrombocytopenia and, in its complete form, also causes small platelets and humoral immunodeficiency. A 14-year-old boy, diagnosed with WAS but never treated, presented with symptoms of heart and renal failure. His right buccal region was swollen and his right first molar showed a cyst-like image on dental X-ray films. The boy's symptoms were attributed to an infected cyst, greatly aggravated by WAS-related immunodeficiency. The boy was sedated and the affected tooth and cyst were enucleated. Invasive treatment was safely achieved by paying close attention to whole-body management.
▸ Wiskott-Aldrich syndrome(WAS) is a congenital X-linked immunodeficiency. ▸ A 14-year-old boy with severe symptoms of cardiac and renal failure. ▸ Large swelling was observed in right buccal region and molar had severe caries. ▸ The affected tooth and cyst were encleated after including deep intravenous sedation. ▸ Platelet transfusions to prevent bleeding and postoperative development of anemia.
Journal: Oral Science International - Volume 10, Issue 1, January 2013, Pages 40–43