Single-Stage Neonatal Repair of Taussig-Bing Anomaly

Taussig-Bing is a form of double outlet right ventricle that is characterized by the presence of subpulmonary ventricular septal defect, double conus and side by side great arteries. Frequently, associated anomalies such as aortic coarctation, arch hypoplasia, subaortic obstruction, and atypical coronary artery anatomy are present; all increasing the complexity of the repair. Advances in perioperative care, perfusion and surgical techniques have allowed the performance of complete repair of Taussig-Bing anomaly with excellent results. Consequently, single stage repair has become the preferred treatment method in most pediatric cardiac centers. Reoperation for right ventricular outflow tract obstruction remains the most common late complication however aggressive resection of the right ventricular muscle bundles creating subaortic obstruction at time of initial repair and reconstruction of the neo pulmonary artery with a generous patch have mitigated that reoperation risk.