Maxillofacial fibrosarcoma arising from dermatofibrosarcoma protuberance: A case report and review

Fibrosarcoma is an infrequent malignant fibroblastic tumor of maxillofacial region, and it can be a rare event in dermatofibrosarcoma protuberance (DFSP). It is locally aggressive but has low incidence of locoregional lymph node and/or distant hematogenous metastases. We report here a case of a 52-year-old Somali woman with a massive tumor on her right maxilla, with repeated recurrences after surgical excision. Histological differentiation of this spindle-shaped tumor cells provide some diagnostic challenges as most of these fibroblastic lesions are lacking specific immunohistochemical markers and typical histomorphological pattern may be absent.The findings of the present case are being discussed with existing literature.