Hipertensión pulmonar del adulto

Pulmonary hypertension (PH) is a hemodynamic and pathophysiological condition that can be associated with various clinical diseases, which have been classified into 5 well-characterized clinical groups based on the latest categorization proposed in Nice in 2013. Pulmonary arterial hypertension (PAH) represents a disease that includes the entities in clinical group I, all of which are clinically similar and share a number of pathological abnormalities identical to those present in pulmonary microcirculation. In the past decade, the availability of new specific pulmonary vasodilator treatments, along with a multidisciplinary approach to the disease in reference centers, has managed to improve the survival of patients with HAP by approximately 20%. Moreover, surgical techniques (lung/heart transplantation/septostomy) have also been improving. A number of these techniques, such as thromboendarterectomy, are potentially curative in selected forms of chronic thromboembolic PH (CTEPH).