Cystic Dysplasia of the Rete Testis: A Case of Spontaneous Regression and Review of Published Reports

Cystic dysplasia of the rete testis (CDT) is a rare benign testicular tumor. We present the second case of spontaneous regression in a 9-year-old boy and summarize the findings of 48 cases in published reports. The most common presentation is scrotal and/or testicular swelling. Common associated renal tract anomalies include ipsilateral renal agenesis and multicystic dysplastic kidney. In 13% of patients, no associated renal anomalies were observed. Orchidectomy was performed in 65% of patients (n = 31) and testicular-sparing surgery, that is, enucleation in 15% (n = 8). In 5 of these 8 patients, recurrence was noted. In a further 12% of patients (n = 5), cystic dysplasia of the rete testis was treated with surveillance. At present, there is no clear consensus on treatment. The conservative approach of “watch and wait” may be supported by this case of spontaneous regression.