Metástasis linfática subcapsular paraaórtica en tumor de los cordones sexuales con diferenciación anular

We present a case of ovarian sex cord tumor with annular tubules not associated with Peutz-Jeghers syndrome and with micrometastasis in a paraaortic node. The tumor was diagnosed as an ultrasonographic finding in a 15-year-old patient who consulted for primary amenorrhea. Unilateral annexectomy was initially performed but, in view of the definitive pathological analysis, a second surgical staging was performed with preservation of the uterus and contralateral adnexa. Postoperative follow-up consisted of periodic ultrasound examination and serum inhibin determinations. After 3 years of follow-up the patient is asymptomatic and disease free, with normal menstrual cycles.