À propos d'un cas évocateur de dystrophie cristalline de Schnyder

Schnyder's crystalline corneal dystrophy is a rare bilateral hereditary disease with various clinical features. It typically presents as a central disc-like opacification with or without crystalline deposits. We report the case of a particular crystalline-free and ring-like pattern dystrophy resembling Schnyder's corneal dystrophy in an 82-year-old woman. In addition, we describe the aspects of this dystrophy with in vivo confocal microscopy using the Heidelberg Retina Tomograph II-Rostock Cornea Module and with anterior segment optical coherence tomography (OCT-Visante®). These techniques can be useful in the diagnosis or the therapeutic process, showing crystalline structures that are not clinically distinguishable or validating the histological localization of the corneal disease.