کد مقاله کد نشریه سال انتشار مقاله انگلیسی نسخه تمام متن
4081740 1267606 2013 6 صفحه PDF دانلود رایگان
عنوان انگلیسی مقاله ISI
Correction of malformative patellar instability in patients with nail-patella syndrome: A case report and review of the literature
موضوعات مرتبط
علوم پزشکی و سلامت پزشکی و دندانپزشکی ارتوپدی، پزشکی ورزشی و توانبخشی
پیش نمایش صفحه اول مقاله
Correction of malformative patellar instability in patients with nail-patella syndrome: A case report and review of the literature
چکیده انگلیسی

SummaryNail-patella syndrome (NPS) or hereditary onycho-osteodysplasia is a relatively rare autosomal dominant disorder with the classic tetrad of fingernail abnormalities, hypoplastic patellae, radial head dislocation and iliac horns. The anatomic abnormalities in NPS often lead to subluxation or dislocation of the patellaeca causing knee instability and pain. Although most existing literature regarding the knee manifestation of this syndrome has focused on the clinically and radiological changes, only a few articles discussed the surgical treatment. This study reports the clinical, radiological and arthroscopical findings and a 24-month follow-up after operative stabilisation considering the underlying pathomorphology of malformative patellar instability in an 11-year-old girl. The findings of this study confirm the unique pathology of NPS with a synovial band preventing the engagement of the patella into the trochlear groove. NPS is a rare disorder and has to be considered in cases with untypical patella dislocation. The underlying pathology differs completely from patients with patellofemoral instability. The aim of orthopaedic surgery should be correction of the underlying pathology with resection of the synovial band and an additional realignment of the patella by recentering of the quadriceps muscle. Considering the underlying pathology good clinical results can be expected.

ناشر
Database: Elsevier - ScienceDirect (ساینس دایرکت)
Journal: Orthopaedics & Traumatology: Surgery & Research - Volume 99, Issue 6, October 2013, Pages 749–754
نویسندگان
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