Cochlear implantation in a bilateral endolymphatic sac tumor patient

At the present time, the optimal management of patients with locally aggressive ELSTs includes: early diagnosis, surgical complete excision and long term follow up to monitor for recurrent disease. The presence of bilateral tumors produces a significant risk for bilateral profound hearing loss. We report the unusual case of bilateral endolymphatic sac tumor in a 14-year-old girl who presented bilateral anacusis and in whom a cochlear implant was performed after removal of the second tumor.