Surgical intervention for Kasaback-Merritt Syndrome: A case report

• Kasabach-Merritt Syndrome is an uncommon phenomenon but can be life threatening.
• Presents with a vascular tumor, thrombocytopenia, coagulopathy and hemodynamic instability.
• Medical treatment consists of steroids, antiplatelets, vincristine, interferon-α, and sirolimus.
• For patients with life or limb threatening tumors, surgical intervention becomes the only viable option.

Kasabach-Merritt Syndrome (KMS) is an uncommon phenomenon characterized by the presence of a vascular tumor in association with thrombocytopenia, consumption coagulopathy and hemodynamic instability. Typically presents in infancy and involve the skin and deep soft tissues of the arms and legs. Treatment options vary with clinical presentation, and ranges from medical management to immediate surgical intervention. We present an unusual case of a newborn with KMS and fatal hemodynamic collapse imminent, which was successfully treated with surgical resection at our institution.