Tubular duplication of colon and terminal ileum in a female child, case report, review of literature and proposal of a new classification

• Think of colon duplication when you see a fistula with a normally situated anus.
• Duplication of anus, external genitals or urinary system points to colon duplication.
• Contrast enema, MCUG, CT Scan and MRI should be done for associated anomalies.
• Treatment should aim at preserving bowel length.
• Cases of colon duplication with absent anus have complex anatomy.

A case of a four and a half years old girl with total colon and terminal ileal duplication with a normally situated anus, vestibular fistula, double bladder and urethra with a unique feature of loop duplication of terminal ileum and part of the colon is reported. A proposal is made for a new simplified classification.