کد مقاله کد نشریه سال انتشار مقاله انگلیسی نسخه تمام متن
6041358 1189286 2015 11 صفحه PDF دانلود رایگان
عنوان انگلیسی مقاله ISI
Workshop report1st Italian SMA Family Association Consensus Meeting:: Management and recommendations for respiratory involvement in spinal muscular atrophy (SMA) types I-III, Rome, Italy, 30-31 January 2015
موضوعات مرتبط
علوم زیستی و بیوفناوری علم عصب شناسی علوم اعصاب تکاملی
پیش نمایش صفحه اول مقاله
Workshop report1st Italian SMA Family Association Consensus Meeting:: Management and recommendations for respiratory involvement in spinal muscular atrophy (SMA) types I-III, Rome, Italy, 30-31 January 2015
چکیده انگلیسی


- This paper reviews and updates recommendations for respiratory care stratified by disease type and severity.
- Specifically the paper describes the management pathway in SMA I at diagnosis and at follow-up.
- Respiratory assessment and follow-up recommendations in SMA II and IIIA.
- Criteria for NIV launching in SMA II and IIIA.
- Secretion management protocols in SMA II and III.

ناشر
Database: Elsevier - ScienceDirect (ساینس دایرکت)
Journal: Neuromuscular Disorders - Volume 25, Issue 12, December 2015, Pages 979-989
نویسندگان
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