کد مقاله کد نشریه سال انتشار مقاله انگلیسی نسخه تمام متن
6217190 1273757 2013 6 صفحه PDF دانلود رایگان
عنوان انگلیسی مقاله ISI
Heterotaxy syndrome and intestinal rotation abnormalities: A survey of institutional practice
موضوعات مرتبط
علوم پزشکی و سلامت پزشکی و دندانپزشکی پریناتولوژی (پزشکی مادر و جنین)، طب اطفال و بهداشت کودک
پیش نمایش صفحه اول مقاله
Heterotaxy syndrome and intestinal rotation abnormalities: A survey of institutional practice
چکیده انگلیسی

PurposeAbnormalities of intestinal rotation (IRA) are commonly associated with heterotaxy syndrome (HS). There is controversy whether asymptomatic infants with HS require screening for IRA and if present, whether a prophylactic Ladd procedure is indicated. The objective of this study is to determine institutional practice across North America in the management of asymptomatic infants with HS and IRA.MethodsWe performed an international, multi-institutional web based survey to examine current practice and opinions in the management of IRA in HS patients.ResultsOverall response rate was 30%. Of physicians surveyed, 84% believe that HS patients should be screened for IRA in the neonatal period. 61% of general surgeons, 50% of cardiovascular surgeons and 45% of cardiologists feel that all patients with HS and an asymptomatic IRA should have a prophylactic Ladd procedure. 55% of physicians stated they would be comfortable with conservative management for patients with HS and asymptomatic IRA.ConclusionsThe risk of midgut volvulus, morbidity and mortality from elective procedures and cardiovascular prognosis must be considered prior to an elective Ladd procedure on asymptomatic HS patients. There are practice variance among sub-specialists caring for these patients, a lack of expert consensus, and a paucity of evidence-based data for IRA in this population.

ناشر
Database: Elsevier - ScienceDirect (ساینس دایرکت)
Journal: Journal of Pediatric Surgery - Volume 48, Issue 10, October 2013, Pages 2078-2083
نویسندگان
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