Hematoma cervical e hemotórax espontâneos no contexto de neurofibromatose tipo I

NF1 is a genetic disorder that rarely can be associated with life‐threatening haemorrhage. The vasculopathy is an underestimated complication with limited recognition in NF1. The excessive vascular friability with spontaneous bleeding in NF1 is rare and can be fatal, requiring a timely diagnosis and prompt treatment.