کد مقاله کد نشریه سال انتشار مقاله انگلیسی نسخه تمام متن
8662383 1576090 2018 7 صفحه PDF دانلود رایگان
عنوان انگلیسی مقاله ISI
Common presentation of rare diseases: Arrhythmogenic right ventricular cardiomyopathy and its mimics
ترجمه فارسی عنوان
معرفی مشترک بیماری های نادر: کاردیومیوپاتی بطنی آریتومنیک و تقلید آن
موضوعات مرتبط
علوم پزشکی و سلامت پزشکی و دندانپزشکی کاردیولوژی و پزشکی قلب و عروق
چکیده انگلیسی
Arrhythmogenic right ventricular cardiomyopathy (ARVC) is the most common phenotype described within the spectrum of arrhythmogenic cardiomyopathies. It usually presents in early adolescence with severe ventricular arrhythmias along with cardiac structural and functional alterations mainly of the right ventricular myocardium. Though the estimated prevalence of ARVC in the general population is only 1:5000, it represents one of the most common causes of juvenile sudden death. However, detection of early RV dysfunction in ARVC may be challenging requiring high clinical suspicion and an algorithmic approach. A thorough family history of juvenile sudden death, ventricular arrhythmias and ICD implants should always be sought. Diagnosis usually requires electrocardiographic interpretation as well as cardiac imaging. In this article, the key diagnostic steps in the assessment of ARVC and diagnostic red flags that aid its differential diagnosis are discussed.
ناشر
Database: Elsevier - ScienceDirect (ساینس دایرکت)
Journal: International Journal of Cardiology - Volume 257, 15 April 2018, Pages 371-377
نویسندگان
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