Uveopapillitis due to Behcet's disease in a patient with Waardenburg syndrome

Waardenburg syndrome is a rare congenital plurimalformatif syndrome combining mainly ocular, auditory, and dermatological lesions. This syndrome is due to developmental abnormalities of melanocytes during embryogenesis. Behcet's disease is a systemic vasculitis of arterial or venous vessels of different sizes. The association with Waardenburg syndrome appears to be incidental. We report a case of a unilateral uveopapillitis related to Behcet's disease in a patient with Waardenburg syndrome type II. The association between Behcet's disease and Waardenburg syndrome has never been described in the literature, which may lead this case report to be a front-runner in the description of a new Waardenburg syndrome type.