Second primary rhabdomyosarcoma of the uterine cervix presenting with synchronous ovarian Sertoli-Leydig cell tumor: An illustrative case of DICER1 syndrome

- Embryonal rhabdomyosarcoma of the uterine cervix and ovarian Sertoli-Leydig cell tumors are associated with DICER1 mutation
- DICER1-associated tumors should prompt genetic counseling and testing
- Somatic and germline genetic mutation profiles can be used to differentiate second primary from recurrent tumors