Atrophie essentielle de l'iris associée à un œdème maculaire cystoïde chronique

We describe a first clinical case associating progressive essential iris atrophy (iridocorneal epithelial syndrome, or ICE syndrome) and chronic cystoid macular edema. The clinical presentation and therapeutic progression suggest an inflammatory retinal barrier rupture as seen in Irvine-Gass syndromes. OCT or angiographic exploration should be systematically performed in cases of ICE syndrome to detect a subclinical macular edema.