Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Quantitative sensory testing (QST); Skin biopsy; Nerve biopsy; Axonal swelling;
مقالات ISI اسکلروز جانبی جانبی آمیوتروفیک (ALS) (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Event-related potentials (ERP); Executive functions; Error(-related) negativity (Ne/ERN); Cognitive impairment; ACC; anterior cingulate cortex; ALS; amyotrophic lateral sclerosis; ALSFRS-R; ALS functional rating scale
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Profilin 1 (PFN1); ALS-causing C71G mutation; Aggregation; Membrane-interacting protein; NMR spectroscopy;
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); amyotrophic lateral sclerosis (ALS); neurodegeneration; motor neuron diseases; drug development; genomics
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Brain-Machine Interface (BMI); Amyotrophic lateral sclerosis (ALS); Spinal cord injury (SCI); Stroke; Augmentative and assistive communication (AAC); Adaptive classification; ALS; amyotrophic lateral sclerosis; BCI; brain-computer interface; LDA; linear d
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Apparent diffusion coefficient (ADC); 3 T brain magnetic resonance imaging (MRI); Intracranial corticospinal tracts; Cervical spondylotic myelopathy (CSM)
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Magnetic resonance spectroscopy (MRS); Diffusion tensor imaging (DTI); ALS functional rating scale-revised (ALSFRS-R); Disease progression rate; Corticospinal tract (CST)
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Fused-in-sarcoma (FUS); Amyotrophic lateral sclerosis (ALS); Frontotemporal dementia (FTD); Valocin-containing protein (VCP); Metabolic; Protein degradation;
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Motor neuron disease (MND); Neurodegeneration; Diagnostic criteria; Neuromuscular disease;
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Decomposition-based quantitative electromyography (DQEMG); Decomposition-enhanced spike-triggered averaging (DE-STA); Motor unit number estimation (MUNE); Reliability; Trapezius muscle; Amyotrophic lateral sclerosis (ALS)
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Dimethyl labeling quantitative proteomics; Mass spectrometry (MS); Muscle biopsy;
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Optineurin (OPTN); Autophagy; Ubiquitin–proteasome system (UPS); Normal tension glaucoma (NTG); Amyotrophic lateral sclerosis (ALS); Autophagy receptor; Autophagy inducer; Protein aggregate; Mitophagy; Tumor suppressor; Aggrephagy; Xenophagy
ATP enhances at low concentrations but dissolves at high concentrations liquid-liquid phase separation (LLPS) of ALS/FTD-causing FUS
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Liquid-liquid phase separation (LLPS); Fused in sarcoma (FUS); Amyotrophic lateral sclerosis (ALS); Frontotemporal dementia (FTD); Adenosine triphosphate (ATP); NMR spectroscopy;
TDP-43 NTD can be induced while CTD is significantly enhanced by ssDNA to undergo liquid-liquid phase separation
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); TDP-43; Liquid-liquid phase separation (LLPS); Ubiquitin-like fold; Prion-like domain; Single-stranded DNA (ssDNA);
Motor neuron differentiation of iPSCs obtained from peripheral blood of a mutant TARDBP ALS patient
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic Lateral Sclerosis (ALS); Induced Pluripotent Stem Cells (iPSCs); Peripheral blood; TDP43; Motor neuron;
Detection of the suspected neurotoxin β-methylamino-l-alanine (BMAA) in cyanobacterial blooms from multiple water bodies in Eastern Australia
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); β-methylamino-l-alanine (BMAA); Non-protein amino acid (NPAA); 2,4-Diaminobutyric acid (2,4-DAB); Amyotrophic lateral sclerosis (ALS); Motor neuron disease (MND); Algal toxin;
Mutation screening of NEK1 in Chinese ALS patients
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); NEK1; Loss-of-function mutation;
NEK1 genetic variability in a Belgian cohort of ALS and ALS-FTD patients
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Frontotemporal dementia (FTD); NIMA-related kinase 1; NEK1;
The accumulation of enzymatically inactive cuproenzymes is a CNS-specific phenomenon of the SOD1G37R mouse model of ALS and can be restored by overexpressing the human copper transporter hCTR1
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Motor neurone disease; Neurodegeneration; Mouse model; Superoxide dismutase 1 (SOD1); Ceruloplasmin; Cytochrome c oxidase (CCO); Copper transporter 1 (CTR1); Copper; Diacetyl-bis(4-methylthiosemicarbazonato)copperII [C
High frequency of C9orf72 hexanucleotide repeat expansion in amyotrophic lateral sclerosis patients from two founder populations sharing the same risk haplotype
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); C9orf72; Cohort studies;
Hippo, Drosophila MST, is a novel modifier of motor neuron degeneration induced by knockdown of Caz, Drosophila FUS
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); ALS; amyotrophic lateral sclerosis; Caz; Cabeza; CNS; central nervous system; DAPI; 4,6-diamino-2-phenylidole dihydrochloride; FALS; familial amyotrophic lateral sclerosis; FUS; Fused in Sarcoma; hpo; Hippo; HRP; horseradish peroxidase; MST; Mammalian ste
ALS-associated mutation SOD1G93A leads to abnormal mitochondrial dynamics in osteocytes
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); ALS; Amyotrophic lateral sclerosis; Drp1; dynamin-related protein 1; G93A; an ALS mouse model with overexpression of ALS-associated mutation SOD1G93A; GFP; green fluorescence protein; OPA1; optic atrophy protein 1; SOD1; superoxide dismutase 1; SOD1G93A;
Astrocyte elevated gene-1 is a novel regulator of astrogliosis and excitatory amino acid transporter-2 via interplaying with nuclear factor-κB signaling in astrocytes from amyotrophic lateral sclerosis mouse model with hSOD1G93A mutation
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); ALS; Amyotrophic lateral sclerosis; AEG-1; Astrocyte elevated gene-1; ACM; astrocyte-conditioned medium; CBP; CREB-binding protein; COX-2; Cyclooxygenase-2; DMSO; dimethyl sulfoxide; DL-NBP; DL-3-n-butylphthalide; DMEM; Dulbecco modified Eagle medium; EAA
Altered CSF cytokine network in amyotrophic lateral sclerosis patients: A pathway-based statistical analysis
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Neuroinflammation; Cytokines; Network; Pathway-based method;
ALS-causing cleavages of TDP-43 abolish its RRM2 structure and unlock CTD for enhanced aggregation and toxicity
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); TDP-43; Inter-domain interactions; ALS-Causing cleavage; C-terminal domain (CTD); NMR spectroscopy;
The alteration of serine transporter activity in a cell line model of amyotrophic lateral sclerosis (ALS)
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Motor neuron disease; d-Serine; l-Serine;
Investigating the role of ALS genes CHCHD10 and TUBA4A in Belgian FTD-ALS spectrum patients
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Frontotemporal dementia (FTD); CHCHD10; TUBA4A;
An easy method for bacterial expression and purification of wild-type and mutant superoxide dismutase 1 (SOD1)
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); SOD1; Amyotrophic lateral sclerosis (ALS); Aggregation; Oligomers; Amyloid; Enzyme activity;
A multi-matrix HILIC-MS/MS method for the quantitation of endogenous small molecule neurological biomarker N-acetyl aspartic acid (NAA)
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); N-Acetyl-aspartic acid (NAA); Biomarker; Human plasma and cerebrospinal fluid (CSF); Hilic-ms/ms; Supported liquid extraction (SLE); Amyotrophic lateral sclerosis (ALS);
An efficient method for analysis of EMG signals using improved empirical mode decomposition
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Electromyography (EMG); Improved empirical mode decomposition (IEMD); Impulsive noise; Median filter;
Modeling ALS and FTD with iPSC-derived neurons
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Induced pluripotent stem cells (iPSCs); Amyotrophic lateral sclerosis (ALS); Frontotemporal dementia (FTD); Frontotemporal lobar degeneration (FTLD);
Inter-domain interactions of TDP-43 as decoded by NMR
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Frontotemporal dementia (FTD); TDP-43; Inter-domain interaction; Prion-like domain; NMR spectroscopy;
SALS-linked WT-SOD1 adopts a highly similar helical conformation as FALS-causing L126Z-SOD1 in a membrane environment
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Superoxide dismutases 1 (SOD1); Membrane-interacting protein; Amphiphilicity; Hydrophobicity; NMR spectroscopy;
SOD1 in neurotoxicity and its controversial roles in SOD1 mutation-negative ALS
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Familial amyotrophic lateral sclerosis (FALS); Sporadic amyotrophic lateral sclerosis (SALS); Cu,Zn superoxide dismutase (SOD1); Neurodegeneration; Motor neuron;
Mechanisms of FUS mutations in familial amyotrophic lateral sclerosis
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); RNA binding protein; Fused in sarcoma (FUS); Prion-like property; Low complexity domain; DNA damage repair; RNA splicing; Amyotrophic lateral sclerosis (ALS); Frontotemporal dementia (FTD);
TDP-43 regulates endogenous retrovirus-K viral protein accumulation
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Endogenous retrovirus (ERVK); TAR DNA-binding protein 43 (TDP-43); Autophagy; Stress granule; Amyotrophic lateral sclerosis (ALS);
TBK1 mutation frequencies in French frontotemporal dementia and amyotrophic lateral sclerosis cohorts
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); TBK1; Frontotemporal dementia (FTD); Amyotrophic lateral sclerosis (ALS); Frontotemporal lobar degeneration (FTLD); Optineurin; Loss of function;
VCP mutations are not a major cause of familial amyotrophic lateral sclerosis in the UK
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Familial ALS (FALS); Valosin containing protein (VCP); Inclusion body myopathy with Paget's disease of bone and fronto-temporal dementia (IBMPFD); Frontotemporal dementia (FTD); Paget's disease of bone (PDB); Hexanucle
ZnII(atsm) is protective in amyotrophic lateral sclerosis model mice via a copper delivery mechanism
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Copper/zinc-superoxide dismutase (SOD1); Therapeutic; Copper; Zinc; Mouse model; Bisthiosemicarbazone (btsc); Metal; Inductively coupled plasma mass spectrometry (ICP-MS); Transmetallation;
Experimental approaches for elucidating co-agonist regulation of NMDA receptor in motor neurons: Therapeutic implications for amyotrophic lateral sclerosis (ALS)
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); d-Serine; d-Amino acid oxidase (DAO); Amyotrophic lateral sclerosis (ALS); Motor neurons; Glycine
Preliminary evaluation of the sensitivity to change of DE-STA motor unit number estimation in the upper trapezius muscle in amyotrophic lateral sclerosis
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Decomposition-based quantitative electromyography (DQEMG); Decomposition-enhanced spike-triggered averaging (DE-STA); Motor unit number estimation (MUNE); Trapezius muscle; Amyotrophic lateral sclerosis (ALS); Sensitivity to change;
Mechanism for transforming cytosolic SOD1 into integral membrane proteins of organelles by ALS-causing mutations
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Superoxide dismutase 1 (SOD1); Membrane protein; Amphiphilicity; NMR spectroscopy
Regular ArticleSuppression of adenosine 2a receptor (A2aR)-mediated adenosine signaling improves disease phenotypes in a mouse model of amyotrophic lateral sclerosis
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Adenosine; A2a receptor; KW6002; Astrocyte; Motor neuron; Amyotrophic lateral sclerosis (ALS);
Mesenchymal stromal cells loading curcumin-INVITE-micelles: A drug delivery system for neurodegenerative diseases
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Mesenchymal stromal cells; Inulin; Vitamin E; Curcumin; Amyotrophic lateral sclerosis (ALS)
Modeling amyotrophic lateral sclerosis in pure human iPSc-derived motor neurons isolated by a novel FACS double selection technique
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Motor neuron disease; Amyotrophic lateral sclerosis (ALS); Induced pluripotent stem cells (iPSc); Cell death; Axon degeneration; Fluorescent-activated cell sorting (FACS); p75NTR; HB9; Superoxide dismutase 1 (SOD1);
De novo FUS mutations are the most frequent genetic cause in early-onset German ALS patients
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Early onset; Fused in sarcoma (FUS); De novo mutation; Genetic testing;
P300-based brain-computer interface (BCI) event-related potentials (ERPs): People with amyotrophic lateral sclerosis (ALS) vs. age-matched controls
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Brain-computer interface (BCI); Alternative and augmentative communication (AAC); Event-related potentials (ERP); Amyotrophic lateral sclerosis (ALS); Brain-machine interface (BMI); Electroencephalography (EEG);
Screening of CHCHD10 in a French cohort confirms the involvement of this gene in frontotemporal dementia with amyotrophic lateral sclerosis patients
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Frontotemporal lobar degeneration (FTLD); Frontotemporal dementia (FTD); Amyotrophic lateral sclerosis (ALS); CHCHD10; Mitochondrial disease;
Deuteration and fluorination of 1,3-bis(2-phenylethyl)pyrimidine-2,4,6(1H,3H,5H)-trione to improve its pharmacokinetic properties
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); ADME; absorption, distribution, metabolism, excretion; ALS; amyotrophic lateral sclerosis; PYT; pyrimidine 2,4,6-trione; Pyrimidine-2,4,6-triones (PYT); Amyotrophic lateral sclerosis (ALS); Fluorination; Deuteration; ADME; Microsome stability; Pharmacokin
Quantitative assessment of hsp70, IL-1β and TNF-α in the spinal cord of dogs with E40K SOD1-associated degenerative myelopathy
Keywords: اسکلروز جانبی جانبی آمیوتروفیک (ALS); Amyotrophic lateral sclerosis (ALS); Canine; Heat shock protein 70 (hsp70); Neuroinflammation; Superoxide dismutase-1 (SOD-1);