Keywords: CF; Cystic fibrosis; CGD; Chronic granulomatous disease; COPD; Chronic obstruction pulmonary disease; CRS; Chronic rhinosinusitis; CVID; Common variable immunodeficiency; PAD; Primary antibody deficiency; PIDD; Primary immunodeficiency disease; TMP-SMX; T
مقالات ISI (ترجمه نشده)
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در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: CGD; Chronic granulomatous disease; Reduced-intensity conditioning regimen for CGD;
Keywords: Flow cytometry; Intracellular protein; Monoclonal antibody; Primary immunodeficiency disease; Surface protein; ADA; adenosine deaminase; ALPS; autoimmune lymphoproliferative syndrome; APECED; autoimmune polyendocrinopathy-candidiasis-ectodermal dystrop
Keywords: WES; IBD; Neutrophil Oxidative Burst; Genetic Variant; ATP; adenosine triphosphate; CADD; Combined Annotation-Dependent Depletion; CD; Crohn's disease; CGD; chronic granulomatous disease; FMLP; N-formyl-methionyl-leucyl-phenylalanine; GM-CSF; granulocyt
Keywords: APC; antigen presenting cell; CGD; chronic granulomatous disease; DC; dendritic cell; FcγR; Fc gamma receptor; GILT; γ-interferon-inducible lysosomal thiol reductase; GPI; glucose-6-phosphate isomerase; HEL; hen egg lysozyme; IFN-γ; interferon-gamma; I
Keywords: CGD; Primary immunodeficiency; Molecular diagnosis; HSCT;
Keywords: CG; coagulating gland; CGd; coagulating gland duct; CGRP; calcitonin gene-related peptide; Dd; deferent duct; Ed; ejaculatory duct; MG; mucous gland; PG; prostate gland; PGd; prostate gland duct; PS; pubic symphysis; SC; seminal colliculus; SV; seminal ve
Keywords: Hematopoietic stem cell transplantation; gammaretroviral vector; lentiviral vector; gene editing; site-specific endonuclease; zinc finger nuclease; CRISPR/Cas9; ADA-SCID; Adenosine deaminase-deficient severe combined immunodeficiency; CGD; Chronic granu
Keywords: Epithelium; Microbiota; Inflammation; Hypoxia-Inducible Factor; Metabolism; ATP; adenosine triphosphatase; CGD; chronic granulomatous disease; DMOG; dimethyloxalylglycine; GI; gastrointestinal; HIF; hypoxia-inducible factor; IBD; inflammatory bowel diseas
Keywords: Glucose-6-phosphate dehydrogenase deficiency; chronic granulomatous disease; neutrophil extracellular trap formation; innate immunity; immunodeficiency; NADPH; CGD; Chronic granulomatous disease; DHR; Dihydrorhodamine 123; G6P; Glucose-6-phosphate; G6PD;
Keywords: Immunology; primary immunodeficiency; whole-exome sequencing; hematopoietic stem cell transplantation; common variable immunodeficiency; severe combined immunodeficiency; hyper-IgE syndrome; AIP1; Actin-interacting protein 1; APDS; Activated PI3Kδ syndro
Keywords: Chronic granulomatous disease; inflammatory manifestations; mammalian target of rapamycin inhibition; autophagy; inflammasome; IL-17A; IL-1β; APC; Allophycocyanin; CGD; Chronic granulomatous disease; DMSO; Dimethyl sulfoxide; FITC; Fluorescein isothiocya
Keywords: CGD; chronic granulomatous disease; CYBB; cytochrome b beta chain; fMLP; formyl-methionyl-leucyl-phenylalanine; NMD; Nonsense-mediated decay; NOX; NADPH oxidase; PAF; platelet-activating factor; PMA; phorbol-myristate acetate; (P)ESE; (putative) exonic sp
Keywords: Primary immunodeficiency; Adults; CGD; Chronic granulomatous disease; CVID; Common variable immune deficiency; HSCT; Hematopoietic stem cell transplant; IVIG; Intravenous immunoglobulin; PID; Primary immune deficiency;
Keywords: Chronic granulomatous disease; hyperinflammation; hematopoietic stem cell; dysfunctional hematopoiesis; competitive repopulation assay; engraftment defect; cell cycle; IL-1β; anakinra; gene therapy; BM; Bone marrow; BrdU; 5-Bromo-2â²-deoxyuridine; CFU;
Keywords: Database Analysis; GI; Intestine; Disease Phenotype; CGD; chronic granulomatous disease; GI; gastrointestinal; IBD; inflammatory bowel disease; NIH; National Institutes of Health; ROS; reactive oxygen species;
Keywords: CGD; Granulocyte function; NADPH; Flow cytometry; Autosomal recessive
Keywords: ALPS; Autoimmune lymphoproliferative syndrome; AT; Ataxia telangiectasia; CD; Complement deficiency; CGD; Chronic granulomatous disease; CHH; Cartilage-hair hypoplasia; CHS; Chediak-Higashi syndrome; CMC; Chronic mucocutaneous candidiasis; CN; Cyclic
Keywords: Immunology; primary immunodeficiency; dedicator of cytokinesis 8; HIV1; recombination-activating gene 1; intravenous immunoglobulin; common variable immunodeficiency; severe combined immunodeficiency; newborn screening; ADA; Adenosine deaminase; ApoE; Apo
Keywords: Primary immune deficiency; microscopy; cell biology; cytoskeleton; host defense; AP3; Adaptor protein 3; Arp2/3; Actin-related proteins 2 and 3; CDC42; Cell division cycle 42; CGD; Chronic granulomatous disease; CHS; Chediak-Higashi syndrome; CTL; Cytotox
Keywords: BTK; Bruton tyrosine kinase; CGD; chronic granulomatous disease; CMC; chronic mucocutaneous candidiasis; γc; γ-common; HLH; hemophagocytic lymphohistiocytosis; HSCT; hematopoietic stem cell transplantation; ITK; IL2-inducible T cell kinase; NK; natural
Keywords: BAL; bronchoalveolar lavage; CFU; colony forming units; CGD; chronic granulomatous disease; ELA; neutrophil elastase; IA; invasive aspergillosis; NADPH; nicotinamide dinucleotide phosphate; NET; neutrophil extracellular trap; PMN; polymorphonuclear neutro
Keywords: NET; neutrophil extracellular trap; IDO; indoleamine 2,3-dioxygenase; CF; cystic fibrosis; CGD; chronic granulomatous disease; ROS; reactive oxygen species; RLU; relative luminescence unit; CFU; colony-forming unit; AhR; aryl hydrocarbon receptor; HRPO; h
Keywords: Immunology; primary immunodeficiency; nuclear factor κB; autoimmunity; intravenous immunoglobulin; common variable immunodeficiency; severe combined immunodeficiency; newborn screening; gene therapy; ADA; Adenosine deaminase; ADAM; A disintegrin and meta
Impaired X-CGD T cell compartment is gp91phox-NADPH oxidase independent
Keywords: CGD; Chronic Granulomatous Disease; NADPH; Nicotinammide adenina dinucleotide fosfato; TCR; T-cell reception; ROS; Reactive oxygen species; PBMC; Peripheral blood mononuclear cells; SIN-LVV; Self-inactivating lentiviral vector; CGD; T lymphocytes; TCRV-be
X-linked carriers of chronic granulomatous disease: Illness, lyonization, and stability
Keywords: Superoxide; X inactivation; dihydrorhodamine flow cytometry test; autoimmunity; lyonization; AIM; Autoimmune or inflammatory manifestation; CGD; Chronic granulomatous disease; DHR; Dihydrorhodamine 123; DLE; Discoid lupus erythematous; NADPH; Reduced nico
The proinflammatory effects of macrophage-derived NADPH oxidase function in autoimmune diabetes
Keywords: ABIS; All Babies in Southwest Sweden study; APC; Antigen presenting cells; Arg-1; Arginase 1; CB3; Coxsackievirus strain B3; CB4; Coxsackievirus strain B4; CGD; Chronic granulomatous disease; CSF-1; Colony-stimulating factor 1; AISY; Diabetes Autoimmunity
Conversion of NOX2 into a constitutive enzyme in vitro and in living cells, after its binding with a chimera of the regulatory subunits
Keywords: AA; all-cis-Arachidonic Acid; CCCP; carbonyl cyanide 3-chlorophenyl hydrazone; CGD; Chronic Granulomatous Disease; cyt c; cytochrome c; cyt b558; flavocytochrome b558; DPI; Diphenylene Iodonium; DISCO; Dichroism, Imaging and mass Spectrometry for Chemical
Polyamine- and NADPH-dependent generation of ROS during Helicobacter pylori infection: A blessing in disguise
Keywords: 8-OHdG; 8-hydroxy-2-deoxyguanosine; ABL1; ABL proto-oncogene 1; AhpC; alkyl hydroperoxide reductase; AKT1; V-Akt murine thymoma viral oncogene homolog 1; APEX1; endonuclease apurinic/apyrimidinic endodeoxyribonuclease 1; ARG1; arginase 1; ARG2; arginase 2
Down-regulation of NOX2 activity in phagocytes mediated by ATM-kinase dependent phosphorylation
Keywords: NOX; NADPH oxidase; ROS; reactive oxygen species; CGD; chronic granulomatous disease; PMA; Phorbol 12-myristate 13-acetate; fMLP; formyl-methionylleucyl-phenylalanine; DMF; dimethylformamide; DFP; diisopropylfluorophosphate; DPI; diphenylene iodonium; INT
CYBA encoding p22phox, the cytochrome b558 alpha polypeptide: gene structure, expression, role and physiopathology
Keywords: CYBA; p22phox; NADPH oxidase; NOX; CGD; polymorphism; vascular
Mechanistic aspects of the formation of α-dystroglycan and therapeutic research for the treatment of α-dystroglycanopathy: A review
Keywords: α-DG; Glycosyltransferase; O-Mannose glycan; Ribitol 5-phosphate; Antisense therapy; Fukuyama congenital muscular dystrophy; α-DG; alpha-dystroglycan; FCMD; Fukuyama type congenital muscular dystrophy; MEB; muscle eye brain disease; WWS; Walker Warburg
Immune deficiencies, infection, and systemic immune disordersMycobacterial disease in patients with chronic granulomatous disease: AÂ retrospective analysis of 71 cases
Keywords: Mycobacteria; BCG; chronic granulomatous disease; tuberculosis; primary immunodeficiency; AR; Autosomal recessive; CGD; Chronic granulomatous disease; EM; Environmental mycobacteria; MSMD; Mendelian susceptibility to mycobacterial disease; NADPH; Nicotina
Seroprofiling at the Candida albicans protein species level unveils an accurate molecular discriminator for candidemia
Keywords: AU; arbitrary units; BSI; bloodstream infection; CI; confidence interval; CGD; Candida Genome Database; HCA; hierarchical cluster analysis; IC; invasive candidiasis; OR; odds ratio; PCA; principal component analysis; PMF; peptide mass fingerprinting; PTM;
NMDA receptors control vagal afferent excitability in the nucleus of the solitary tract
Keywords: CIQ; (3-chlorophenyl)(6,7-dimethoxy-1-((4-methoxyphenoxy)methyl)-3,4-dihydroisoquinolin-2(1H)-yl)methanone; CGD; CalciumGreen 1-dextran; d,l-AP5; d,l-2-amino-5-phosphonopentanoic acid; mEPSCs; miniature postsynaptic excitatory currents; NST; nucleus of th
Defective B-cell proliferation and maintenance of long-term memory in patients with chronic granulomatous disease
Keywords: Chronic granulomatous disease; B cell; proliferation; long-term memory; measles; memory B-cell compartment; reactive oxygen species deficiency; Anti-Ig; F(abâ²)2 fragment goat anti-human IgA+IgG+IgM; ASC; Antibody-secreting cell; BCR; B-cell receptor; CG
Neutrophil NET formation is regulated from the inside by myeloperoxidase-processed reactive oxygen species
Keywords: CGD; chronic granulomatous disease; CL; chemiluminescence; DAG; sn-1,2-dioctanoylglycerol; DPI; diphenyleneiodonium; HRP; horseradish peroxidase; KRG; Krebs-Ringer phosphate buffer; MPO; myeloperoxidase; NETs; neutrophil extracellular traps; PEG; polyethy
Pioglitazone restores phagocyte mitochondrial oxidants and bactericidal capacity in chronic granulomatous disease
Keywords: Chronic granulomatous disease; phagocytes; mitochondria; oxidants; thioglitazones; BADGE; Bisphenol AÂ diglycidyl ether; CFU; Colony-forming units; CGD; Chronic granulomatous disease; DHR; Dihydrorhodamine; DPI; Diphenylene iodonium; mtROS; Mitochondrial
Dermatology grand rounds at the NIHRecurrent erythematous plaques on sun-exposed sites in an African American boy with chronic granulomatous disease
Keywords: chronic granulomatous disease; discoid lupus erythematosus; drug reaction; lupuslike eruption; photoeruption; phototoxicity; voriconazole; CGD; chronic granulomatous disease; DLE; discoid lupus erythematosus; PAS-D; periodic acid-Schiff diastase; TMP-SMX;
Uric acid induces NADPH oxidase-independent neutrophil extracellular trap formation
Keywords: CGD; chronic granulomatous disease; DHR; dihydrorhodamine 123; DPI; diphenyleneiodonium; HBSS; Hanks' balanced salt solution; MSU; monosodium urate; MVP; trans-1-(2â²-methoxyvinyl)pyrene; Nox; NADPH oxidase; NET; neutrophil extracellular trap; PBN; α-
A Candida albicans PeptideAtlas
Keywords: SRM; Selected Reaction Monitoring; CGD; Candida Genome Database; FDR; False Discovery Rate; PSM; Peptide-Spectrum Match; PRIDE; Protein Identifications Database; PSS; Predicted Suitability Score; ESS; Empirical Suitability Score; Candida albicans; Pepti
Detection of superoxide anion and hydrogen peroxide production by cellular NADPH oxidases
Keywords: CGD; chronic granulomatous disease; cpYFP; circularly permutated form of the yellow fluorescent protein; DCFH2; dihydrofluorescein; DH2R; dihydrorhodamine; DUOX; dual oxidase (1 or 2); DUOXA; dual oxidase maturation factor (1 or 2); fMLF; formyl methionyl
ReviewMendelian susceptibility to mycobacterial disease: Genetic, immunological, and clinical features of inborn errors of IFN-γ immunity
Keywords: AD; autosomal dominant; AR; autosomal recessive; BCG; bacillus Calmette-Guérin; CGD; chronic granulomatous disease; CMC; chronic mucocutaneous candidiasis; EM; environmental mycobacteria; GOF; gain-of-function; HSCT; hematopoietic stem cell transplantati
Reviews and PerspectivesReviews in Basic and Clinical Gastroenterology and HepatologyThe Diagnostic Approach to Monogenic Very Early Onset Inflammatory Bowel Disease
Keywords: Inflammatory Bowel Disease; Crohn's Disease; Ulcerative Colitis; Unclassified Colitis; Indeterminate Colitis; Immunodeficiency; Pediatrics; IBD Unclassified; Genetics; Next-Generation Sequencing; Whole Exome Sequencing; CD; Crohn's disease; CGD; chron
Eosinophilic cystitis in the pediatric population: AÂ case series and review of the literature
Keywords: Eosinophilic cystitis; Pediatric; Inflammation; Bladder; VUR; vesicoureteral reflux; CIC; clean intermittent catheterization; CGD; chronic granulomatous disease; EC; eosinophilic cystitis; WBC; white blood cells;
B-cell activating factor (BAFF) is elevated in Chronic Granulomatous Disease
Keywords: CGD; Chronic Granulomatous Disease; BCR; B cell receptor; BAFF; B cell activating factor; TACI; transmembrane activator and CAML-interactor.; Chronic Granulomatous Disease; B-cell activating factor; Inflammation;
Gene therapy for PIDs: Progress, pitfalls and prospects
Keywords: PIDs; primary immunodeficiency disorders; HSCs; haematopoietic stem cells; ADA-SCID; adenosine deaminase deficiency-severe combined immunodeficiency; SCID-X1; X-linked severe combined immunodeficiency; CGD; chronic granulomatous disorder; WAS; Wiskott-A
A negative role for MyD88 in the resistance to starvation as revealed in an intestinal infection of Drosophila melanogaster with the Gram-positive bacterium Staphylococcus xylosus
Keywords: AMP; antimicrobial peptides; CGD; chronic granulomatous disease; DIF; Dorsal-related immunity factor; FOXO; forkhead box O; GNBP3; Gram-negative protein 3; IMD; Immune deficiency; ISC; intestinal stem cell; IRC; Immune-regulated catalase; JAK/STAT; Janus
Antibiotic Prophylaxis in Primary Immune Deficiency Disorders
Keywords: Primary immune deficiency diseases; Immunodeficiency; Antibody deficiency syndromes; Antibiotic prophylaxis; AAAAI; American Academy of Allergy, Asthma, and Immunology; AOM; Acute otitis media; BAT; Bronchiectasis and Long-term Azithromycin Treatment; CF;
Diagnosis and Treatment of Gastrointestinal Disorders in Patients With Primary Immunodeficiency
Keywords: Immune System; Hypogammaglobulinemia; IBD; Inflammatory Intestinal Disease; 6-MP; mercaptopurine; AZA; azathioprine; CGD; chronic granulomatous disease; CVID; common variable immunodeficiency; FOXP3; forkhead box P3; GI; gastrointestinal; GVHD; graft-vers