
Keywords: CPET، تست ورزش قلبی عروقی; CF, cystic fibrosis; CFTR, cystic fibrosis transmembrane conductance regulator; CPET, cardiopulmonary exercise test; Db10, potentiated doublets at 10 Hz; Db100, potentiated doublets at 100 Hz; Db10:100, ratio between potentiated doublets at 10 Hz and 100