
Sodium phenylbutyrate reverses lysosomal dysfunction and decreases amyloid-β42 in an in vitro-model of inclusion-body myositis
Keywords: الیاف عضلانی انسان کشت شده است; Aβ42; amyloid beta 42; AD; Alzheimer disease; Baf; bafilomycin A1; CHMFs; cultured human muscle fibers; Chl; chloroquine; HDAC; histone deacetylase; iNOS; inducible nitric oxide synthase; NaPB; sodium phenylbutyrate; PD; Parkinson disease; s-IBM; sporadi