
Experimental evidence of oxidative stress in patients with l-2-hydroxyglutaric aciduria and that l-carnitine attenuates in vitro DNA damage caused by d-2-hydroxyglutaric and l-2-hydroxyglutaric acids
Keywords: L-2-HGA; l-2-hydroxyglutaric aciduria; L-2-HG; l-2-hydroxyglutaric acid; D-2-HGA; d-2-hydroxyglutaric aciduria; D-2-HG; d-2-hydroxyglutaric acid; 2-HG; 2-hydroxyglutaric acid; LC; l-carnitine; L2HGDH; l-2-hydroxyglutarate dehydrogenase gene; D2HGDH; d-2-h