Keywords: دیسمولیناسین; hypocholesterolemia (Oita); cholesterol metabolism; intractable epilepsy; hypogonadism; cerebro-cerebellar-bulbar degeneration; dysmyelination
مقالات ISI دیسمولیناسین (ترجمه نشده)
مقالات زیر هنوز به فارسی ترجمه نشده اند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: دیسمولیناسین; Leukodystrophy; Inborn error of metabolism; Dysmyelination; Demyelination; Spectroscopy; White matter;
Brain magnetic resonance imaging findings and auditory brainstem response in a child with spastic paraplegia 2 due to a PLP1 splice site mutation
Keywords: دیسمولیناسین; Spastic paraplegia 2; Pelizaeus–Merzbacher disease; PLP1; Dysmyelination; Auditory brainstem response
Phenotypic characterization of a Csf1r haploinsufficient mouse model of adult-onset leukodystrophy with axonal spheroids and pigmented glia (ALSP)
Keywords: دیسمولیناسین; ALSP; adult-onset leukoencephalopathy with axonal spheroids and pigmented glia; CSF-1R; colony stimulating factor-1 receptor; FA; fractional anisotropy; GFAP; glial fibrillary acidic protein; G-CSF; granulocyte-CSF; GM-CSF; granulocyte macrophage-CSF; HDL
Three-dimensional ultra-structures of myelin and the axons in the spinal cord: Application of SEM with the osmium maceration method to the central nervous system in two mouse models
Keywords: دیسمولیناسین; EAE; experimental autoimmune encephalomyelitis; MBP; myelin basic protein; MOG; myelin oligodendrocyte glycoprotein; Myelin morphology; Dysmyelination; Demyelination;
Sequential neuroradiological and neurophysiological studies in a Japanese girl with merosin-deficient congenital muscular dystrophy
Keywords: دیسمولیناسین; Merosin-deficient congenital muscular dystrophy; Laminin α2; Dysmyelination; Demyelination
Oligodendroglial pathology in the development of myelin breakdown in the dmy mutant rat
Keywords: دیسمولیناسین; Dysmyelination; Mutant rat; Oligodendrocyte; Oligodendrocyte progenitor cell; MitochondriaCNS, central nervous system; OPCs, oligodendrocyte progenitor cells; PLP, proteolipid protein
High b-value and diffusion tensor imaging in a canine model of dysmyelination and brain maturation
Keywords: دیسمولیناسین; Diffusion tensor imaging; q-Space; High b-value; Radial diffusivity; Restricted diffusion; Myelin; Axons; Dysmyelination; Brain development;
Head trauma can initiate the onset of adreno-leukodystrophy
Keywords: دیسمولیناسین; Adreno-leukodystrophy; Adrenomyeloneuropathy; Head trauma; Long chain fatty acids; Demyelination; Dysmyelination; White matter
A study of the reproducibility and etiology of diffusion anisotropy differences in developmental stuttering: A potential role for impaired myelination
Keywords: دیسمولیناسین; Developmental stuttering; Radial diffusivity; Myelogenesis; Superior longitudinal fasciculus; Dysmyelination;
Ventilatory impairment in the dysmyelinated Long Evans shaker rat
Keywords: دیسمولیناسین; myelin basic protein; dysmyelination; phrenic motor output; ventilation; plethysmography; hypercapnia; f; breathing frequency; FICO2; inspiratory fraction of carbon dioxide; FIO2; inspiratory fraction of oxygen; les; Long Evans shaker rat; mbp; myelin bas
Cell-specific loss of κ-opioid receptors in oligodendrocytes of the dysmyelinating jimpy mouse
Keywords: دیسمولیناسین; Proteolipid protein; Pelizaeus–Merzbacher disease; Dysmyelination; Cell death; Corpus callosum; Striatum
Effects of osmolality on PLP-null myelin structure: Implications re axon damage
Keywords: دیسمولیناسین; Demyelination; Dysmyelination; Proteolipid protein; Pelizaeus–Merzbacher disease; Spastic paraplegia type 2; Multiple sclerosis
Discrepancy between auditory brainstem responses, auditory steady-state responses, and auditory behavior in two patients with Pelizaeus-Merzbacher disease
Keywords: دیسمولیناسین; Pelizaeus-Merzbacher disease; Dysmyelination; ABR; ASSR; Auditory behavior;
Shah-Waardenburg syndrome and PCWH associated with SOX10 mutations: A case report and review of the literature
Keywords: دیسمولیناسین; Shah-Waardenburg syndrome; PCWH; SOX10-mutations; Demyelinating; Dysmyelination; Case report; Review
Statistical diffusion tensor histology reveals regional dysmyelination effects in the shiverer mouse mutant
Keywords: دیسمولیناسین; Dysmyelination; Shiverer mutant; Magnetic resonance microscopy; Diffusion tensor imaging