Keywords: FAP، polyneuropathy آمیلوئیدوتی فامیلی; ALP, alkaline phosphatase; ATTR, amyloidogenic transthyretin; FAP, familial amyloidotic polyneuropathy; LT, liver transplantation; SELDI-TOF MS, surface-enhanced laser desorption/ionization time-of-flight mass spectrometry; SeV, Sendai virus; TTR, transth
مقالات ISI FAP، polyneuropathy آمیلوئیدوتی فامیلی (ترجمه نشده)
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Impact of antibodies against amyloidogenic transthyretin (ATTR) on phenotypes of patients with familial amyloidotic polyneuropathy (FAP) ATTR Valine30Methionine
Keywords: FAP، polyneuropathy آمیلوئیدوتی فامیلی; TTR, transthyretin; FAP, familial amyloidotic polyneuropathy; ATTR, amyloidogenic transthyretin; V30M, Valine30Methionine; PBS, phosphate-buffered saline; OD, optical density; AD, Alzheimer's diseaseAntibody against amyloidogenic transthyretin V30M; Famil
Wild-type transthyretin-derived amyloidosis in various ligaments and tendons
Keywords: FAP، polyneuropathy آمیلوئیدوتی فامیلی; SSA, senile systemic amyloidosis; FAP, familial amyloidotic polyneuropathy; TTR, transthyretin; β2-m, β2-microglobulin; SELDI, surface-enhanced laser desorption/ionization; DRA, dialysis-related amyloidosisSenile systemic amyloidosis; Ligament; Tendon; Am
Cardiac autonomic function does not improve after liver transplantation for familial amyloidotic polyneuropathy
Keywords: FAP، polyneuropathy آمیلوئیدوتی فامیلی; ATTR, Amyloidogenic transthyretin; ECG, Electrocardiogram; FAP, Familial amyloidotic polyneuropathy; HF, High frequency; HRV, Heart rate variability; LF, Low frequency; MET, Methionine; TTR, Transthyretin; VAL, ValineHRV; Heart rate variability; Amyloid;
Impact of serotonin transporter and catechol-O-methyl transferase genes polymorphism on gastrointestinal dysfunction in Swedish and Japanese familial amyloidotic polyneuropathy patients
Keywords: FAP، polyneuropathy آمیلوئیدوتی فامیلی; FAP, familial amyloidotic polyneuropathy; ATTR, amyloidogenic transthyretin; Val30Met, Valine30Methionine; 5-HTTLPR, serotonin transporter gene-linked polymorphic region; COMT, catechol-O-methyl transferase; IBS, irritable bowel syndrome; PCR, polymerase
Cholesterol and anionic phospholipids increase the binding of amyloidogenic transthyretin to lipid membranes
Keywords: FAP، polyneuropathy آمیلوئیدوتی فامیلی; Aβ, β-amyloid protein; AFM, atomic force microscopy; DLS, dynamic light scattering; ER, endoplasmic reticulum; FAP, familial amyloidotic polyneuropathy; HOPG, highly oriented pyrolytic graphite; KD, dissociation constant; PC, dimyristoyl-l-α-phosphatidylc
In vitro inhibition of transthyretin aggregate-induced cytotoxicity by full and peptide derived forms of the soluble receptor for advanced glycation end products (RAGE)
Keywords: FAP، polyneuropathy آمیلوئیدوتی فامیلی; AGE, advanced glycation end products; FAP, familial amyloidotic polyneuropathy; HMGB-1, high mobility group box 1 protein or amphoterin; RAGE, receptor for AGE; RBP, retinol-binding protein; sRAGE, soluble RAGE; TTR, transthyretinTransthyretin; Receptor f
Retention of Misfolded Mutant Transthyretin by the Chaperone BiP/GRP78 Mitigates Amyloidogenesis
Keywords: FAP، polyneuropathy آمیلوئیدوتی فامیلی; BiP; misfolding; intermediate; amyloid; oligomerCNS, central nervous system; CSF, cerebrospinal fluid; TTR, transthyretin; FAP, familial amyloidotic polyneuropathy; ER, endoplasmic reticulum; Hsp, heat shock protein; D18G, mutant with an aspartate to glyc