Keywords: Multiple sulfatase deficiency; Leukodystrophy; Mucopolysaccharidoses; Consensus; Therapy; Care; Outcomes; Prevention; ACC; augmentative and alternative communication; AEP; auditory evoked potential; BiPAP; bilevel positive airway pressure; CPAP; continuou
مقالات ISI (ترجمه نشده)
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در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: Akt2; RAC-β serine/threonine-protein kinase; AR; aldose reductase; Bcl-2; B-cell lymphoma 2; CFL1; cofilin 1;; cMDH1; cytosolic NAD-dependent malate dehydrogenase 1; CTSK; cathepsin K; Cu-Zn SOD; Cu/Zn superoxide dismutase; DHAR2; dehydroascorbate reduct
Keywords: 4-OH-TEMPO; 4-hydroxy-2,2,6,6-tetramethylpiperidinyloxy; AAPBA; N-acryloyl-m-aminophenyl boronic acid; ABS; acrylonitrile-butadiene-styrene copolymer; AFM; atomic force microscopy; AIBN; 2,2-azodiisobutyronitrile; AOBA; 4-allyloxybenzaldehyde; APBA; 4-ami
Keywords: Self-healing polymers; Self-repair; Autonomous healing; Polymer composites; BDMA; benzyl-N,N-dimethylamine; CAI; compression after impact; CoNp; cobalt naphtenate; CT; compact tension; CuAAC; Cu(I)-catalyzed azide-alkyne cycloaddition; DBTL; di-n-butyltin
Población y metodologÃa del estudio SIMETAP: Prevalencia de factores de riesgo cardiovascular, enfermedades cardiovasculares y enfermedades metabólicas relacionadas
Keywords: Dislipidemia; Enfermedad cardiovascular; Factores de riesgo; Prevalencia; SÃndrome metabólico; Dyslipidaema; Cardiovascular disease; Risk factors; Prevalence; Metabolic syndrome; ACV; Enfermedad o accidente cerebrovascular, ictus; ADA; American Diabetes
Crystal structure of PvdO from Pseudomonas aeruginosa
Keywords: Pseudomonas aeruginosa; Crystal structure; PvdO; FGE;
Anaerobic sulfatase maturase AslB from Escherichia coli activates human recombinant iduronate-2-sulfate sulfatase (IDS) and N-acetylgalactosamine-6-sulfate sulfatase (GALNS)
Keywords: Cys; Cysteine; FGly; Formylglycine; GALNS; N-acetylgalactosamine-6-sulfate sulfatase; GALNSSer; GALNS cDNA containing mutation C79S; IDS; iduronate-2-sulfate sulfatase; MPS; Mucopolysaccharidoses; anSMEs; Anaerobic sulfatase maturating enzymes; SUMF1; Sul
Choline sulfatase from Ensifer (Sinorhizobium) meliloti: Characterization of the unmodified enzyme
Keywords: COS; E. meliloti choline-O-sulfatase; FGly; α-formylglycine; FGE; α-formylglycine-generating enzyme; anSME; anaerobic sulfatase maturing enzyme; pNPS; p-nitrophenyl sulfate; MUS; 4-methylumbelliferyl sulfate; ITC; isothermal titration calorimetry; DLS;
Developing treatment options for metachromatic leukodystrophy
Keywords: ARSA; arylsulfatase A; LSD; lysosomal storage disease; MLD; metachromatic leukodystrophy; HSCT; hematopoietic stem cell transplantation; UCBT; umbilical cord blood transplantation; MSCT; mesenchymal stem cell transplantation; ERT; enzyme replacement thera
Seguimiento durante 36 meses de la función renal en el anciano
Keywords: ERC; Anciano; FGe; Función renal; CKD; Elderly; eGFR; Renal function;
First evidences for a third sulfatase maturation system in prokaryotes from E. coli aslB and ydeM deletion mutants
Keywords: Sulfatase; Radical SAM; Radical AdoMet; AnSME; Formylglycine; FGE
Valor pronóstico de la creatinina sérica en el sÃndrome coronario agudo sin elevación del segmento ST
Keywords: Pronóstico; Isquemia miocárdica; Insuficiencia renal; Prognosis; Myocardial ischemia; Kidney failure; FGE; filtrado glomerular estimado; MDRD; modification of diet in renal disease; RI; rango intercuartil; SCA; sÃndrome coronario agudo; SCASEST; sÃndr