Keywords: فوماریلا آتوآستات هیدرولاز; Arginase deficiency; Hyperargininemia; Ammonia; Urea cycle disorder; Treatment; Cellular transplant; FAH; fumarylacetoacetate hydrolase; FRG; Fahâ/â/Rag2â/â/Il2rγâ/â mouse; CKO; conditional knockout; NTBC; 2-(2-nitro-4-trifluoromethylbenzoyl)
مقالات ISI فوماریلا آتوآستات هیدرولاز (ترجمه نشده)
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در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: فوماریلا آتوآستات هیدرولاز; Mouse Model; Regeneration; Signal Transduction; CYP7A; BAC; bacterial artificial chromosome; BDL; bile duct ligation; FAH; fumarylacetoacetate hydrolase; FGF; fibroblast growth factor; FXR; farnesoid X receptor; NPC; nonparenchymal cell; PCR; polymerase c
Keywords: فوماریلا آتوآستات هیدرولاز; Hepatocyte; Liver; Chimera; Humanization; Animal Model; AFC8; FKBP-Caspase 8 gene driven by the albumin promoter; CYP; cytochrome; Fah; fumarylacetoacetate hydrolase; FRG; Fah/Rag2/interleukin common gamma chain knockout; NOD; non-obese diabetic; NTBC; 2-
Mildly elevated succinylacetone and normal liver function in compound heterozygotes with pathogenic and pseudodeficient FAH alleles
Keywords: فوماریلا آتوآستات هیدرولاز; Tyrosinemia; Hypersuccinylacetonemia; Fah; Fumarylacetoacetate hydrolase; Nitisinone; Pseudodeficiency;
In vivo gene correction with targeted sequence substitution through microhomology-mediated end joining
Keywords: فوماریلا آتوآستات هیدرولاز; In vivo gene correction; Microhomology-mediated end-joining (MMEJ); Targeted sequence substitution (TSS); Hereditary tyrosinemia; Homology-directed repair (HDR); HDR; Homology-directed repair; NHEJ; Non-homologous end-joining; MMEJ; Microhomology-mediate
Diagnosis and therapy with CRISPR advanced CRISPR based tools for point of care diagnostics and early therapies
Keywords: فوماریلا آتوآستات هیدرولاز; CRISPR; clustered regularly interspaced short palindromic repeats; Cas; CRISPR-associated protein; crRNA; CRISPR RNA; SgRNA; single guide RNA; tracrRNA; trans-activating RNA; PAM; protospacer-adjacent motif; DSB; DNA double strand break; SHERLOCK; Specifi
Research ArticleIron overload in hereditary tyrosinemia type 1 induces liver injury through the Sp1/Tfr2/hepcidin axis
Keywords: فوماریلا آتوآستات هیدرولاز; HTI; hereditary tyrosinemia type I; Fah; fumarylacetoacetate hydrolase; Tfr2; transferrin receptor 2; HH; hereditary hemochromatosis; Hjv; hemojuvelin; NTBC; 2-(2-nitro-4-trifluoromethylbe -nzoyl)-1,3-cyclohexanedione; Fpn; ferroportin; Tfr1; transferrin
Advances in therapeutic CRISPR/Cas9 genome editing
Keywords: فوماریلا آتوآستات هیدرولاز; Cas9; CRISPR-associated protein 9; cccDNA; covalently closed circular DNA; CCR5; chemokine receptor 5; CFTR; cystic fibrosis transmembrane conductance regulator; CRISPRs; clustered regularly interspaced short palindromic repeats; crRNA; CRISPR RNA; Crygc;
Effect of nitisinone (NTBC) treatment on the clinical course of hepatorenal tyrosinemia in Québec
Keywords: فوماریلا آتوآستات هیدرولاز; AFP; alpha-foetoprotein; ALA; delta-aminolevulinic acid; ALT; alanine aminotransferase; FAH; fumarylacetoacetate hydrolase; HT1; hereditary tyrosinemia, type 1; 4HPL; 4-hydroxyphenyllactate; 4HPP; 4-hydroxyphenylpyruvate; PBG; porphobilinogen; SA; succiny
Induction of a mature hepatocyte phenotype in adult liver derived progenitor cells by ectopic expression of transcription factors
Keywords: فوماریلا آتوآستات هیدرولاز; ALDPC; adult liver-derived progenitor cells; iPS; induced pluripotent stem cells; LETF; liver enriched transcription factors; LD; liver differentiation medium; HBM; hepatocyte basal medium; MM; maintenance medium; ESC; embryonic stem cells; Foxa2; forkhea
Rescue of Lethal Hepatic Failure by Hepatized Lymph Nodes in Mice
Keywords: فوماریلا آتوآستات هیدرولاز; Liver Transplantation; Liver Regeneration; Ectopic Organogenesis; Cell Therapies; Fah; fumarylacetoacetate hydrolase; HGF; hepatocyte growth factor; NTBC; 2-(2-nitro-4-trifluoromethylbenzoyl)-1,3 cyclohexanedione; OLT; orthotopic liver transplantation; SP
Hepatoblast-Like Progenitor Cells Derived From Embryonic Stem Cells Can Repopulate Livers of Mice
Keywords: فوماریلا آتوآستات هیدرولاز; Hepatic Differentiation; Bipotency; Cell Transplantation; Liver Injury; Aat; α1-antitrypsin; Afp; α-fetoprotein; Alb; albumin; BSA; bovine serum albumin; CDM; chemically defined medium; DE; definitive endoderm; DMEM; Dulbecco's modified Eagle medium; ES
The autoimmune response induced by mouse hepatitis virus A59 is expanded by a hepatotoxic agent
Keywords: فوماریلا آتوآستات هیدرولاز; Mouse hepatitis virus; Autoimmune response; Autoimmune hepatitis; Fumarylacetoacetate hydrolase
Rescue from neonatal death in the murine model of hereditary tyrosinemia by glutathione monoethylester and vitamin C treatment
Keywords: فوماریلا آتوآستات هیدرولاز; Hereditary tyrosinemia type 1; Fumarylacetoacetate hydrolase; Glutathione; NTBC
The peptide specificities of the autoantibodies elicited by mouse hepatitis virus A59
Keywords: فوماریلا آتوآستات هیدرولاز; Mouse hepatitis virus; Autoantibody; Autoimmune response; Molecular mimicry; Danger model; Fumarylacetoacetate hydrolase
Effect of low-molecular-weight heparin on the commitment of bone marrow cells to liver sinusoidal endothelial cells in CCl4-induced liver injury
Keywords: فوماریلا آتوآستات هیدرولاز; BMCs; bone marrow cells; CCl4; carbon tetrachloride; DS; dalteparin sodium; FAH; fumarylacetoacetate hydrolase; GFP; green fluorescent protein; HE; hematoxylin eosin; HGF; hepatocyte growth factor; PBS; phosphate-buffered saline; TRITC; tetramethylrhodami
Enzymes of tyrosine catabolism in Arabidopsis thaliana
Keywords: فوماریلا آتوآستات هیدرولاز; Fumarylacetoacetate hydrolase; Glutathione transferase (zeta); Homogentisate dioxygenase; Maleylacetoacetate isomerase; Senescence; Microarray expression analysis;
DNA damage and repair in mammalian cells exposed to p-hydroxyphenylpyruvic acid
Keywords: فوماریلا آتوآستات هیدرولاز; Tyrosinemia; p-Hydroxyphenylpyruvic acid; Fumarylacetoacetate hydrolase; DNA damage; DNA repair; Comet assay; Formamidopyrimidine DNA glycosylase; Endonuclease III; Oxidative stress; Hepatocytes; Hepatocarcinoma;