Keywords: آنژیوادم ارثی; Angioedema without wheals; Nonhistaminergic angioedema; Hereditary angioedema; Idiopathic angioedema; Clinical characteristic; Angioedematous attack; C1-INH-HAE; Hereditary angioedema with C1-inhibitor deficiency; FXII-HAE; Hereditary angioedema with fact
مقالات ISI آنژیوادم ارثی (ترجمه نشده)
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Keywords: آنژیوادم ارثی; Angioedema; Bradykinin; ACE inhibitors; ARBs (angiotensin receptor blockers); Dipeptidyl peptidase IV inhibitors; Neprilysin inhibitors; Icatibant; ACEi; Angiotensin-converting-enzyme inhibitor; ANP; A-type natriuretic peptide; APP; Aminopeptidase P; ARB;
Keywords: آنژیوادم ارثی; Hereditary angioedema; Icatibant; Home-based treatment; Bradykinin-receptor antagonist; AE; Adverse event; HAE; Hereditary angioedema; HCP-administration; Administration by health care professionals at medical facilities; ISR; Injection-site reaction; PSS
Keywords: آنژیوادم ارثی; Hereditary angioedema; Bradykinin; C1 inhibitor deficiency; Bradykinin B2 receptor antagonist; Icatibant; Children; Adolescents; Pediatrics; Treatment; AE; adverse event; C1-INH; C1 inhibitor; C1-INH-HAE; hereditary angioedema with C1-inhibitor deficiency
Keywords: آنژیوادم ارثی; Hereditary angioedema; Complement system; C1-inhibitor; Bradykinin; Mutation;
Keywords: آنژیوادم ارثی; Hereditary angioedema; Hereditary angioedema attacks; Treatment plan; Angioedema management; Emergency department; Angioedema guidelines; On-demand treatment; Patient-reported outcomes; Quality of life; Disease burden; ED; Emergency department; FDA; Food
Keywords: آنژیوادم ارثی; Pharmacoeconomics; Orphan disease; Hereditary angioedema; Burden; Treatment;
Keywords: آنژیوادم ارثی; Contact system; Hereditary angioedema; C1 inhibitor; Bradykinin; C4; C1 inhibitor complexes; Vascular permeability;
Keywords: آنژیوادم ارثی; Prophylaxis; Hereditary angioedema; Androgens; Tranexamic acid; Progestagens; C1 inhibitor;
Keywords: آنژیوادم ارثی; Hereditary angioedema; HAE acute attacks; Treatment of HAE; C1-inhibitor concentrate; Icatibant; Ecallantide; rh C1-INH;
Keywords: آنژیوادم ارثی; Angioedema; Bradykinin; Histamine; Hereditary angioedema;
Keywords: آنژیوادم ارثی; Acquired angioedema; General anesthesia; Hereditary angioedema;
Keywords: آنژیوادم ارثی; Hereditary angioedema; angioedema attack; human C1-inhibitor; efficacy; complement system; contact system; BK; Bradykinin; B1R; Bradykinin receptor 1; B2R; Bradykinin receptor 2; C1INH; C1-inhibitor; CPM; Carboxypeptidase M; CPN; Carboxypeptidase N; FXI;
Keywords: آنژیوادم ارثی; Pediatric hereditary angioedema; Hereditary angioedema; Age onset; C1-INH; C1 inhibitor; CCHMC; Cincinnati Children's Hospital Medical Center; EMR; Electronic medical records; ER; Emergency room; HAE; Hereditary angioedema; IQR; Interquartile range; pdC1I
Keywords: آنژیوادم ارثی; Hereditary angioedema; C1 Inhibitor deficiency; Hereditary angioedema with normal C1 inhibitor activity; Autoimmune diseases; Lupus erythematosus, cutaneous; Lupus erythematosus, systemic;
Keywords: آنژیوادم ارثی; Deep neck infection; Retropharyngeal abscess; Ludwig angina; Peritonsillar abscess; Supraglottitis; Hereditary angioedema; ACE inhibitor angioedema; Allergic angioedema;
Keywords: آنژیوادم ارثی; Anaphylaxis; mast cell; bradykinin; mouse models; tryptase; contact system; ACE; Angiotensin-converting enzyme; Anti-Xa; Anti-factor Xa activity; aPTT; Activated partial thromboplastin time; Bdkrb1; B1R coding gene; Bdkrb2; B2R coding gene; B1R; Bradyki
Keywords: آنژیوادم ارثی; Angioedema ereditario; Chirurgia orale; Immunologia; Edema facciale; Paziente a rischio; Hereditary angioedema; Oral surgery; Immunology; Facial edema; Risk outpatient;
Keywords: آنژیوادم ارثی; Urticaria; Ordinary; Physical; Hereditary angioedema; Pregnancy; Labor; Delivery;
Keywords: آنژیوادم ارثی; Urticaria; Angioedema; Histamine; Bradykinin; Hereditary angioedema; Acquired angioedema; C1 esterase inhibitor; Factor XII gene mutations;
A missense mutation in the plasminogen gene, within the plasminogen kringle 3 domain, in hereditary angioedema with normal C1 inhibitor
Keywords: آنژیوادم ارثی; Hereditary angioedema; Plasminogen; Kringle domain; C1 inhibitor; Coagulation factor XII; Missense mutation;
Health-Related Quality of Life with Subcutaneous C1-Inhibitor for Prevention of Attacks of Hereditary Angioedema
Keywords: آنژیوادم ارثی; C1-inhibitor protein; Hereditary angioedema; Patient-reported outcomes; Quality of life; Productivity; Satisfaction; Subcutaneous; HAEGARDA; C1-INH; C1-inhibitor; C1-INH-HAE; Hereditary angioedema with C1-inhibitor deficiency; CI; Confidence interval; EQ-
Hereditary Angioedema with Normal C1 Inhibitor and F12 Mutations in 42 Brazilian Families
Keywords: آنژیوادم ارثی; Hereditary angioedema; Normal C1 inhibitor; F12 mutations; Estrogen; Brazilian population; ACEI; Angiotensin-converting enzyme inhibitor; C1-INH; C1 inhibitor; C1-INH-HAE; Hereditary angioedema with C1 inhibitor deficiency; eOC; Estrogen-containing oral c
The Journal of Allergy and Clinical Immunology: In Practice 2017 Year in Review
Keywords: آنژیوادم ارثی; Angioedema; Allergy; Asthma; Anaphylaxis; Atopic dermatitis; Contact dermatitis; Drug allergy; Eosinophilic esophagitis; Eosinophilia; Food allergy; Immunodeficiency; Immunotherapy; Rhinitis; Rhinosinusitis; Urticaria; AAAAI; American Academy of Allergy A
Mutation of the angiopoietin-1 gene (ANGPT1) associates with a new type of hereditary angioedema
Keywords: آنژیوادم ارثی; Hereditary angioedema; angiopoietin-1; gene; mutation; multimers; tunica interna endothelial cell kinase 2 receptor; ANGPT1; Angiopoietin-1; ANGPT2; Angiopoietin-2; C1-INH; C1 inhibitor; C1-INH-HAE; Hereditary angioedema caused by C1 inhibitor deficiency;
A novel prophylaxis with C1-inhibitor concentrate in hereditary angioedema during erythema marginatum
Keywords: آنژیوادم ارثی; C1-inhibitor; C1-INH; C1-INH-HAE; hereditary angioedema with C1-inhibitor deficiency; EM; erythema marginatum; HAE; hereditary angioedema; mg; milligram; pdC1-INH; plasma-derived C1-inhibitor; C1-inhibitor deficiency; Erythema marginatum; Hereditary angio
Diminished capacity of opsonization and immune complex solubilization, and detection of anti-C1q antibodies in sera from patients with hereditary angioedema
Keywords: آنژیوادم ارثی; Anti-C1q antibody; Autoimmune disease; Hereditary angioedema; Immune complex; Phagocytosis; C1-INH; C1 esterase inhibitor; CR; Complement receptor; HAE; Hereditary angioedema; IC; Immune complex; NHPS; Normal human pooled sera; PBS; Phosphate buffered sal
Recombinant Human C1-Esterase Inhibitor to Treat Acute Hereditary Angioedema Attacks in Adolescents
Keywords: آنژیوادم ارثی; C1-esterase; Hereditary angioedema; Adolescent; Safety; Efficacy; Ruconest; Pharmacokinetics; AE; Adverse event; C1-INH; C1-esterase inhibitor; Cmax; Maximum concentration; HAE; Hereditary angioedema; IV; Intravenous; OLE; Open-label extension; RCT; Rando
Cytokine and estrogen stimulation of endothelial cells augments activation of the prekallikrein-high molecular weight kininogen complex: Implications for hereditary angioedema
Keywords: آنژیوادم ارثی; Hereditary angioedema; C1 inhibitor; bradykinin; heat shock protein 90; APMSF; (4-Amidinophenyl)-methanesulfonyl fluoride; HAE; Hereditary angioedema; HK; High molecular weight kininogen; PAI-2; Plasminogen activator inhibitor-2; TPA; Tissue plasminogen a
Hereditary Angioedema with Normal C1 Inhibitor
Keywords: آنژیوادم ارثی; Hereditary angioedema; Factor XII; Plasmin; Mutation; Bradykinin; C1-inhibitor;
C1-esterase inhibitor for short-term prophylaxis in a patient with hereditary angioedema with normal C1 inhibitor function
Keywords: آنژیوادم ارثی; Hereditary angioedema; Type III; Normal C1-esterase; HAE-nC1INH; Perioperative; Prophylaxis;
C1-inhibitor efficiently delays clot development in normal human whole blood and inhibits Escherichia coli-induced coagulation measured by thromboelastometry
Keywords: آنژیوادم ارثی; aPTT; activated partial thromboplastin time; C1-INH; C1-inhibitor; E. coli; Escherichia coli; EXTEM; extrinsic thromboelastometry; HAE; hereditary angioedema; HSA; human serum albumin; INTEM; intrinsic thromboelastometry; LI; lysis index; min; minute; NAT
Hereditary angioedema in a Jordanian family with a novel missense mutation in the C1-inhibitor N-terminal domain
Keywords: آنژیوادم ارثی; C1-inhibitor; SERPING1 gene; Hereditary angioedema; Jordan; N-terminal domain
Mechanisms of allergy and clinical immunologyDeficiency of plasminogen activator inhibitor 2 in plasma of patients with hereditary angioedema with normal C1 inhibitor levels
Keywords: آنژیوادم ارثی; Hereditary angioedema; C1 inhibitor; bradykinin; plasminogen activator inhibitor; BCIP/NBT; 5-Bromo-4-chloroindolyl phosphate/nitroblue tetrazolium; C1-INH; C1 inhibitor; HAE; Hereditary angioedema; HAE-N; Hereditary angioedema with normal C1 inhibitor le
Safety and Usage of C1-Inhibitor in Hereditary Angioedema: Berinert Registry Data
Keywords: آنژیوادم ارثی; Berinert; Plasma-derived C1-INH; Patient registry; Thromboembolic event; Real-world; Prophylaxis; On demand; Self-administration; Safety; Dosing; AE; Adverse event; C1-INH; C1 inhibitor; DVT; Deep vein thrombosis; EU; European Union; HAE; Hereditary angio
Psychometric Field Study of Hereditary Angioedema Quality of Life Questionnaire for Adults: HAE-QoL
Keywords: آنژیوادم ارثی; Disease-specific; Quality of life; Hereditary angioedema; C1 inhibitor; Questionnaire; Validation studies; Psychometric; Adults; HAE-QoL; SF-36v2; AE-QoL; Angioedema quality of life questionnaire; C1-INH-HAE; Hereditary angioedema due to C1 inhibitor defi
Tolerability and Effectiveness of 17-α-Alkylated Androgen Therapy for Hereditary Angioedema: A Re-examination
Keywords: آنژیوادم ارثی; 17-α-Alkylated androgen; Hereditary angioedema; Treatment; Effectiveness; Side effects; C1 inhibitor; Severity; Danazol; Prophylaxis; AA; 17-α-Alkylated androgens; C1INH; C1 inhibitor; HAE; Hereditary angioedema; HAE-nl-C1INH; HAE with normal C1 inhibit
Allergenicity and safety of recombinant human C1 esterase inhibitor in patients with allergy to rabbit or cow's milk
Keywords: آنژیوادم ارثی; Hereditary angioedema; recombinant human C1 esterase inhibitor; allergenicity; rabbit allergy; cow's milk allergy; skin prick test; intracutaneous test; intradermal testing; subcutaneous administration; subcutaneous challenge; AE; Adverse event; BAT; Baso
Plasmin is a natural trigger for bradykinin production in patients with hereditary angioedema with factor XII mutations
Keywords: آنژیوادم ارثی; Angioedema; bradykinin; Factor XII; plasma kallikrein; kininogen; C1 esterase inhibitor; plasmin; εACA; ε-Aminocaproic acid; C1inh; C1 esterase inhibitor; FXII; Factor XII; FXIIa; Active Factor XII; HAE; Hereditary angioedema; HBS; HEPES-buffered saline
The autoimmune side of hereditary angioedema: insights on the pathogenesis
Keywords: آنژیوادم ارثی; Autoimmunity; C1 inhibitor; Complement system; Hereditary angioedema; Systemic lupus erythematosus
Comparison of Chromogenic and ELISA Functional C1 Inhibitor Tests in Diagnosing Hereditary Angioedema
Keywords: آنژیوادم ارثی; Hereditary angioedema; C1 inhibitor; Complement testing; C1 INH; C1 inhibitor; HAE; Hereditary angioedema;
ELISA to measure neutralizing capacity of anti-C1-inhibitor antibodies in plasma of angioedema patients
Keywords: آنژیوادم ارثی; NAbs; neutralizing antibodies; C1-inh; C1-inhibitor; AAE; acquired angioedema; HAE; hereditary angioedema; NC%; percentage neutralizing capacity; Auto-autoantibodies; Acquired angioedema; Hereditary angioedema; C1-inhibitor deficiency;
C1-inhibitor polymers activate the FXII-dependent kallikrein-kinin system: Implication for a role in hereditary angioedema
Keywords: آنژیوادم ارثی; BSA; bovine serum albumin; C1-inh; complement C1 esterase inhibitor; C1PIV; in vivo sized C1-inh polymers; CPDA; citrate phosphate dextrose adenine; CPK; chromozyme PK; FXII; coagulation factor XII; FXIIa; activated FXII; dBSA; heat denatured BSA; HAE; he
Recombinant Human-C1 Inhibitor Is Effective and Safe for Repeat Hereditary Angioedema Attacks
Keywords: آنژیوادم ارثی; Hereditary angioedema; Recombinant human C1 esterase inhibitor; Repeat attacks; C1INH; C1 Esterase inhibitor; HAE; Hereditary angioedema; HRI; Host-related impurities; IS; Investigator Score; OLE; Open-label extension; rhC1INH; Recombinant human C1 estera
Characterization of patients with angioedema without wheals: The importance of F12 gene screening
Keywords: آنژیوادم ارثی; C1-INH; C1 inhibitor; HAE; hereditary angioedema; FXII-HAE; hereditary angioedema with factor XII mutation; U-HAE; hereditary angioedema with unknown genetic mutation; InH-AAE; idiopathic non-histaminergic acquired angioedema; SERPING1; serpin peptidase i
Original ArticleCharacterization of Anaphylaxis After Ecallantide Treatment of Hereditary Angioedema Attacks
Keywords: آنژیوادم ارثی; Hypersensitivity; Anaphylaxis; Allergy; Hereditary angioedema; Ecallantide; HAE; -; Negative; +; Positive; Anti-ecal IgE; anti-ecallantide IgE antibody; Anti-P pastoris IgE; anti-P pastoris IgE antibody; bp; Blood pressure; D5W; 5% dextrose in water
Cardiac Surgery and C1-Inhibitor Deficiency
Keywords: آنژیوادم ارثی; hereditary angioedema; cardiac surgery; complement; C1-esterase inhibitor deficiency;
Identification and characterization of a novel splice site mutation in the SERPING1 gene in a family with hereditary angioedema
Keywords: آنژیوادم ارثی; Immunodeficiency;; Hereditary angioedema;; C1-inhibitor;; SERPING1;; Mutation;; Splicing;
Immune deficiencies, infection, and systemic immune disordersEndothelial cell activation during edematous attacks of hereditary angioedema types I and II
Keywords: آنژیوادم ارثی; Hereditary angioedema; C1-inhibitor deficiency; attack; endothelial cells; activation; von Willebrand factor; endothelin-1; soluble E-selectin; clinical study; BMI; Body mass index; C1-INH; C1-inhibitor; C4; Complement factor 4; CRP; C-reactive protein; E
Bradykinin analysis revived – A validated method for determination of its stable metabolite in whole blood by LC–MS/MS
Keywords: آنژیوادم ارثی; Bradykinin; Hereditary angioedema; LC–MS/MS; BK1–5; Validation