
Factors that prognosticate mortality in idiopathic pulmonary arterial hypertension: A systematic review of the literature
Keywords: پرفشاری خون شریانی ریوی ایدیوپاتیک; Idiopathic pulmonary arterial hypertension; Prognosis; Survival; Mortality; Outcomes; Systematic review6MWD, 6 min walk distance; CO, cardiac output; CI, cardiac index; CPET, cardiopulmonary exercise; DLCO, diffusing capacity of carbon monoxide; IPAH, idi