
A fluorescent probe for GM1 gangliosidosis related β-galactosidase: N-(Dansylamino)hexylaminocarbonylpentyl-1,5-dideoxy-1,5-imino-d-galactitol
Keywords: Iminoalditols; d-Galactosidase inhibitor; GM1 gangliosidosis; Pharmacological chaperone; Fluorescent probe