
Keywords: CF, cystic fibrosis; PA, Pseudomonas aeruginosa; HPA, hypermutable Pseudomonas aeruginosa; MDR, multi-drug resistant; FEV1%, forced expiratory volume in 1 s; MEF 25–75%, maximal mid-expiratory flow.Cystic fibrosis; Hypermutable; Pseudomonas aeruginosa