Disruption of the human COQ5-containing protein complex is associated with diminished coenzyme Q10 levels under two different conditions of mitochondrial energy deficiency
Keywords: صرع میوکلونیک با الیاف سرخ شده; 2D BN-PAGE; two-dimensional blue native-polyacrylamide gel electrophoresis; BHA; butylated hydroxyanisole; CoQ; coenzyme Q; FCCP; carbonyl cyanide-p-trifluoromethoxyphenylhydrazone; HPLC; high-performance liquid chromatography; m-COQ5; mature form of COQ5