
Hereditary sensory neuropathy type 1-associated deoxysphingolipids cause neurotoxicity, acute calcium handling abnormalities and mitochondrial dysfunction in vitro
Keywords: âÏm; mitochondrial membrane potential; CHOP; C/EBP homologous protein; CsA; cyclosporine A; DMSp; deoxymethylsphinganine; DRG; dorsal root ganglia; DSp; deoxysphinganine; ER; endoplasmic reticulum; FCCP; carbonyl cyanide-p-trifluoromethoxyphenylhydrazo