
Keywords: PNS، سیستم عصبی محیطی; ARSA, Arylsulfatase A; CNS, central nervous system; EJ, early juvenile; LI, late infantile; MLD, Metachromatic Leukodystrophy; PNS, peripheral nervous system; Pts, patientsMetachromatic Leukodystrophy; Acid–base balance monitoring; Metabolic acidosis; Kid