Keywords: ساپوزین سی; Gaucher disease; Beta-glucocerebrosidase; LIMP-2; Saposin C; Progranulin; Heat shock proteins;
مقالات ISI ساپوزین سی (ترجمه نشده)
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در صورتی که به ترجمه آماده هر یک از مقالات زیر نیاز داشته باشید، می توانید سفارش دهید تا مترجمان با تجربه این مجموعه در اسرع وقت آن را برای شما ترجمه نمایند.
Keywords: ساپوزین سی; ABCA12; ATP-binding cassette transporter A12; α-GalCer; α-galactosylceramide; AMPK; AMP-activated protein kinase; BMP; bis-monoacylglycero-phosphate; CBE; conduritol B epoxide; CerS; ceramide synthase; CERT; ceramide transport protein; ChlGlc; cholester
A rare form of Gaucher disease resulting from saposin C deficiency
Keywords: ساپوزین سی; Gaucher disease; Prosapsin; Saposin C;
Ambroxol-induced rescue of defective glucocerebrosidase is associated with increased LIMP-2 and saposin C levels in GBA1 mutant Parkinson's disease cells
Keywords: ساپوزین سی; PD; Parkinson's disease; GD; Gaucher disease; GCase; glucocerebrosidase; Sap C; saposin C; PSAP; prosaposin; LIMP-2; lysosomal integral membrane 2; ER; endoplasmic reticulum; TFEB; transcription factor EB; GSK3; glycogen synthase kinase 3; UPS; ubiquitin
Selective chaperone effect of aminocyclitol derivatives on G202R and other mutant glucocerebrosidases causing Gaucher disease
Keywords: ساپوزین سی; BBB; blood-brain barrier; CBE; conduritol β-epoxide; Cer; ceramide; D-MEM; Dulbeco Eagle's minimal essential medium; ERT; enzyme replacement therapy; GBA1; lysosomal glucocerebrosidase; GBA2; non-lysosomal glucocerebrosidase; GlcCer; glucosylceramide;
Gaucher disease due to saposin C deficiency, previously described as non-neuronopathic form - No positive effects after 2-years of miglustat therapy
Keywords: ساپوزین سی; Gaucher disease variant; Saposin C; Substrate deprivation therapy; Miglustat;
Synthesis of the sphingolipid activator protein, saposin C, using an azido-protected O-acyl isopeptide as an aggregation-disrupting element
Keywords: ساپوزین سی; Saposin C; O-Acyl isopeptide; Peptide thioester; Native chemical ligation; Azido group;
A mutation in the saposin A coding region of the prosaposin gene in an infant presenting as Krabbe disease: first report of saposin A deficiency in humans
Keywords: ساپوزین سی; Krabbe disease; Sphingolipid activator proteins; Prosaposin; Saposin A; Saposin C; Galactocerebrosidase; Galactosylceramide; Sulphatide loading;
Structural changes in a binary mixed phospholipid bilayer of DOPG and DOPS upon saposin C interaction at acidic pH utilizing 31P and 2H solid-state NMR spectroscopy
Keywords: ساپوزین سی; Sap C; Saposin C; SCD; Molecular Order Parameters; CSA; Chemical Shift Anisotropy; GCase; Glucosylceramidase; CL; Cardiolipin; DOPG; Dioleoylphosphatidylglycerol; DOPS; Dioleoylphosphatidylserine; PC; Phosphoatidyecholines; PG; Phosphatidylglycerol; PS; P
Role of lysine residues in membrane anchoring of saposin C
Keywords: ساپوزین سی; Protein-lipid complex; Saposin C; Phosphatidylserine liposomes; Molecular dynamics simulation; Membrane anchoring;