کد مقاله کد نشریه سال انتشار مقاله انگلیسی نسخه تمام متن
2700804 1144371 2016 9 صفحه PDF دانلود رایگان
عنوان انگلیسی مقاله ISI
Manifestations respiratoires et syndrome d'Ehlers-Danlos (SED) chez l'enfant
موضوعات مرتبط
علوم پزشکی و سلامت پزشکی و دندانپزشکی ارتوپدی، پزشکی ورزشی و توانبخشی
پیش نمایش صفحه اول مقاله
Manifestations respiratoires et syndrome d'Ehlers-Danlos (SED) chez l'enfant
چکیده انگلیسی
Ehlers-Danlos syndrome should not be considered a rare disease, but it nevertheless remains very rarely diagnosed and often too late. Yet, it is essential to make an early diagnosis in order to treat and implement an appropriate special education and daily lifestyle. In children, respiratory events are frequent. The most commonly encountered are: chronic cough, unjustified dyspnea, recurrent bronchitis and finally real asthmatiform dyspnea crisis. The diagnosis is suspected in congenital dislocation of the hip, gastroesophageal reflux (sometimes from the feeding bottle), constipation, bruising, recurrent ear infections, very severe abdominal pains, signs of dysautonomia (nervousness, sweating, cold hands and feet, palpitations and low blood pressure), recurrent sprains, dislocations and subluxations, clumsiness and collisions with objects and falls, a significant hypermobility, dystonia crisis, a thin skin (facilitating the occurrence of electrostatic discharges), very stretchable and brittle with healing disorders and stretch marks, oral manifestations, generally very discreet scoliosis, cognitive difficulties and behavioral psychology. There are effective treatment for early implementation: proprioceptive orthotics (especially compression garments), molded seats, corsets, and Percussionnaire® daily oxygen therapy, preferably local pain, antidystoniques and antidysautonom adapted treatment. Physical activity is essential for the maintenance of proprioception.
ناشر
Database: Elsevier - ScienceDirect (ساینس دایرکت)
Journal: Journal de Réadaptation Médicale : Pratique et Formation en Médecine Physique et de Réadaptation - Volume 36, Issue 1, February 2016, Pages 69-77
نویسندگان
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