Travail musculaire actif et réentraînement à l'effort dans les myopathies

It is now accepted that physical activity is not deleterious in myopathic populations. While there is no cure, physical exercise appears to counteract muscular loss and deconditioning. Current research suggests that well-adapted supervised training programs in myopathic populations lead to improved cardiovascular fitness and psychological health and decreased cardiovascular risk. For this, training must be monitored, adapted and planned by a professional familiar with the physiopathology (e.g. dystrophy, mitochondrial myopathy, myositis) and capacity of the individual patient. Few randomized control trials have been conducted on supervised training programs in myopathic populations and only one followed patients for a year. Thus, myopathy-specific training guidelines are limited because little data exists on which to base recommendations. General consensus indicates that a mixed exercise program combining endurance and strength exercise is more efficient in myopathic populations. In this article, we report the most relevant terms that improve the cardio-respiratory and function capacities and get more psychological benefits and quality of life in the myopathic patient.