The influence of ventricular morphology and coronary artery dominance and morphology on early mortality in patients with pulmonary atresia and intact ventricular septum

Coronary artery abnormalities are known to be present in a certain percentage of patients presenting with pulmonary atresia and intact ventricular septum. These abnormalities range in severity from small fistulae to complete right ventricular dependence of components in the coronary circulation. These abnormalities are known to complicate therapy preoperatively, during palliation, and during definitive correction. This study will explore the influence of right ventricular morphology and coronary artery dominance and morphology on early mortality in infants with pulmonary atresia and intact ventricular septum, something which has not been previously explored.