Management of Neonatal Ebstein’s Anomaly

The presentation of Ebstein’s anomaly (ventricular displacement of the tricuspid valve, especially septal and posterior leaflets) in the neonatal period is distinguished from that in later life by a much higher mortality, due in part to the pre-existing elevation in pulmonary vascular resistance. Surgery in the neonatal period has previously focused on palliation and conversion to single-ventricle physiology. Successful two-ventricle repair with good clinical results can safely be performed in the neonatal period.