کد مقاله | کد نشریه | سال انتشار | مقاله انگلیسی | نسخه تمام متن |
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3966150 | 1256140 | 2014 | 4 صفحه PDF | دانلود رایگان |
IntroductionUterine malformations are a heterogeneous group of congenital anomalies resulting from abnormal development of Mullerian ducts. Herlyn-Werner-Wunderlich syndrome is a rare condition that includes the triad of uterus didelfus, blind hemivagina and ipsilateral renal agenesis. We report a case with premenarche diagnosis and treatment and make a review of the illness.Case reportA premenarche 11 year old female was referred for pediatric nephrology and neurodevelopment consultation due to prenatal diagnosis of left renal agenesis. A pelvic ultrasound was performed and an anomalous uterus and a cystic pelvic mass was incidentally discovered. A 3D trans-rectal ultrasound identified a bicolis didelfus uterus and mucocolpos. A unidigital vaginal exam revealed a single cervix with soft bulging of the left apical vaginal wall. Using monopolar knife, an incision was done allowing drainage of the cavity. A part of the apical vaginal septum was removed and a normal cervix was seen.CommentsA high degree of clinical suspicion is important for the diagnoses. 3D ultrasound or MRI are the imaging diagnostic exams of choice, helped by a careful bimanual pelvic examination. An early diagnosis is important to prevent chronic pelvic pain and perhaps severe endometriosis.
Journal: Middle East Fertility Society Journal - Volume 19, Issue 3, September 2014, Pages 229–232