Embolización selectiva en el manejo prequirúrgico de pseudotumor hemofílico. Reporte de caso y revisión de la bibliografía

Hemophilia A and B are transmitted genetic diseases associated with sex, where the factors VIII and IX are deficient respectively. Its incidence is approximately 1 in 10,000 males born for hemophilia A and 1 in 30,000 for hemophilia B. This deficiency generates bleeding and hematomas that mostly reabsorbed spontaneously. But for unknown reasons, some hematomas are encapsulated and has aggressive growth behavior and local destruction. The hemophilic pseudotumor (PT) is a rare complication that occurs in patients with hemophilia A and B, it is defined as a hemorrhagic encapsulated mass with metabolic activity inside and progressive growth. In some cases, there is a strong relationship with traumatic events. The majority of cases are asymptomatic for long periods, but with the growth, extrinsic compression of other structures and metabolic activity of the tumor inside and outside are painful depending on anatomical site commit. Unfortunately, there is no established protocol for the management of this complication. We report a case of a giant hemophilic pseudotumor thigh treated with selective arterial embolization prior to surgical resection procedure.