Management and treatment of a sialoblastoma of the submandibular gland in a neonate

Objectives: Report a rare congenital salivary gland tumor and its clinical, radiological and histopathologic aspects. Discuss the differential diagnosis and treatment. Methods: A case report is described. A literature review of the incidence, disease course, radiological and histopathologic aspects and treatment are presented. Results: This case report presents a neonate with an asymptomatic left cervical mass. Ultrasounds and MRI showed a circumscribed soft tissue mass measuring 60 mm × 42 mm × 52 mm and extending from the left parotid region to the left submandibular region, but radiological exams could not lead to a diagnosis. A biopsy demonstrated a sialoblastoma. The treatment consisted in a surgical resection with no adjuvant therapy. One year after surgery there is no clinical nor radiological sign of recurrence. Conclusion: Sialoblastomas are rare congenital epithelial salivary tumors and have been reported to occur predominantly in the parotid gland. They are locally aggressive with a high recurrence rate needing a prolonged follow up. When they are completely resectable, surgical resection is the mainstay for treatment of these tumors and no adjuvant therapy is needed.