A rare disorder mimics otitis media in children: Langerhans’ cells histiocytosis

SummaryLangerhans’ cell histiocytosis (LCHs) or histiocytosis X is an idiopathic disorder characterized by a proliferation of histiocytes. It is generally considered to include a spectrum of disorders as eosinophilic granuloma (EG), Hand–Schuller–Christian (HSC) disease and Letterer–Siwe (LS) disease which vary in the prognostic result. EG is the most benign of them. The histiocytic lesions can occur in visceral organ(s) or bone(s) that can lead to presentation of the disease with different clinical manifestations including otologic manifestations. The presence of otorrhea or atypical otitis media, granulation tissue, aural polyps, or a postauricular mass should alert the otolaryngologist to the possibility of LCH. We presented a case of otologic histiocytosis with the temporal bone involvement which mimics as chronic infectious ear disease.