Extraskeletal primary Ewing's sarcoma of the nasal cavity

SummaryEwing's sarcoma (ES) and primitive neuroectodermal tumor represent the most frequent small and round cell bone tumors of childhood and adolescence. ES is the second most common primary malignant tumor of bone in children. In this article, a 1-year-old male patient with ES is presented and recent update on this entity is discussed. Computed tomography (CT) scans of the sinuses revealed a mass that appeared to be originating from the right inferior turbinate and filling the anterior part of the nasal cavity. The patient underwent complete removal of the mass with endoscopic nasal surgery under general anesthesia and was treated with adjuvant chemotherapy. Clinically and radiologically no recurrence of disease was noted during a follow-up period of 1 year. Although ES is extremely rare among nasal cavity neoplasms, it should be considered in the differential diagnosis.