Special airway concerns in patients with mucopolysaccharidoses

SummaryThe mucopolysaccharidoses are comprised of hereditary disorders joined by errant degradation of mucopolysaccharides. The relatively infrequent opportunity to care for these patients is evidenced by a fairly small number of case reports and anecdotal information. Though lifespan is increasing, onset of respiratory pathology or involvement remains portentous. We present two cases that punctuate the need for insightful decision making while managing the airway for these patients